Short stature in partially corrected x-linked severe combined immunodeficiency - Suboptimal response to growth hormone

Journal of Pediatric Endocrinology and Metabolism

Volumn 21, Issue 11, 2008, Pages 1057-1063

  De Ravin, Suk See ^a   Shum, Elaine ^a   Zarember, Kol A ^a   Rezvani, Geoffrey ^b   Rosenfeld, Ron G ^b   Stratakis, Constantine A ^b,c   Malech, Harry L ^a  

^a NATIONAL INSTITUTE OF ALLERGY AND INFECTIOUS DISEASES   (United States)

^b NATIONAL INSTITUTES OF HEALTH   (United States)

^c EUNICE KENNEDY SHRIVER NATIONAL INSTITUTE OF CHILD HEALTH AND HUMAN DEVELOPMENT   (United States)

Author keywords

Growth hormone; IGF I; Short stature; X linked severe combined immunodeficiency; c

Indexed keywords

ACICLOVIR; COTRIMOXAZOLE; FLUCONAZOLE; GROWTH HORMONE; IMMUNOGLOBULIN; INTERLEUKIN 2 RECEPTOR GAMMA; PREDNISONE; RECOMBINANT GROWTH HORMONE; SOMATOMEDIN C;

ADOLESCENT; ALOPECIA; ARTICLE; BONE AGE; BONE MARROW TRANSPLANTATION; CASE REPORT; CELIAC DISEASE; CHRONIC DIARRHEA; DISEASE SEVERITY; DRUG MEGADOSE; DRUG RESPONSE; ENGRAFTMENT; ESOPHAGUS STRICTURE; EX VIVO GENE TRANSFER; GLUTEN FREE DIET; GRAFT VERSUS HOST REACTION; GROWTH DISORDER; GROWTH HORMONE BLOOD LEVEL; HEMOLYTIC ANEMIA; HUMAN; HUMAN CELL; IMMUNE RECONSTITUTION INFLAMMATORY SYNDROME; LOW DRUG DOSE; MALE; PROTEIN BLOOD LEVEL; PROTEIN SYNTHESIS; RASH; RECURRENT INFECTION; RESPIRATORY TRACT INFECTION; SCHOOL CHILD; SHORT STATURE; T CELL DEPLETION; X LINKED SEVERE COMBINED IMMUNODEFICIENCY;

EID: 57849092163     PISSN: 0334018X     EISSN: None     Source Type: Journal    
DOI: 10.1515/JPEM.2008.21.11.1057     Document Type: Article

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