Allogeneic bone marrow transplantation restores IGF-I production and linear growth in a γ-SCID patient with abnormal growth hormone receptor signaling

Bone Marrow Transplantation

Volumn 33, Issue 7, 2004, Pages 773-775

  Salerno, M ^a   Busiello, R ^a   Esposito, V ^a   Cosentini, E ^a   Adriani, M ^a   Selleri, C ^a   Rotoli, B ^a   Pignata, C ^a  

^a UNIVERSITY OF NAPLES FEDERICO II   (Italy)

Author keywords

Growth; Insulin like growth factor I; Severe combined immunodeficiency

Indexed keywords

BUSULFAN; CYCLOPHOSPHAMIDE; CYCLOSPORIN; GROWTH HORMONE; GROWTH HORMONE RECEPTOR; LYMPHOCYTE ANTIBODY; PREDNISONE; SOMATOMEDIN C; THIOTEPA;

ALLOGENIC BONE MARROW TRANSPLANTATION; ARTICLE; CASE REPORT; CELLULAR IMMUNITY; CHILD; CLINICAL FEATURE; COMBINED IMMUNODEFICIENCY; DISEASE SEVERITY; GRAFT VERSUS HOST REACTION; GROWTH CURVE; GROWTH RATE; HEMATOPOIETIC STEM CELL; HUMAN; HUMORAL IMMUNITY; IMMUNOSUPPRESSIVE TREATMENT; MISSENSE MUTATION; PRIORITY JOURNAL; PROTEIN SYNTHESIS; SHORT STATURE; SIGNAL TRANSDUCTION; STEM CELL TRANSPLANTATION; TREATMENT OUTCOME; X CHROMOSOME LINKED DISORDER;

BONE MARROW TRANSPLANTATION; GRAFT SURVIVAL; GROWTH; HUMANS; IMMUNE SYSTEM; IMMUNOGLOBULIN GAMMA-CHAINS; INFANT; INSULIN-LIKE GROWTH FACTOR I; MALE; RECEPTORS, SOMATOTROPIN; REGENERATION; SEVERE COMBINED IMMUNODEFICIENCY; SIGNAL TRANSDUCTION; TRANSPLANTATION, HOMOLOGOUS;

EID: 13444249447     PISSN: 02683369     EISSN: None     Source Type: Journal    
DOI: 10.1038/sj.bmt.1704421     Document Type: Article

References (10)

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