Skeletal and hematological anomalies in HYAL2-deficient mice: A second type of mucopolysaccharidosis IX?

FASEB Journal

Volumn 22, Issue 12, 2008, Pages 4316-4326

  Jadin, Laurence ^a   Wu, Xiaoli ^b   Ding, Hao ^b   Frost, Gregory I ^c   Onclinx, Cécile ^a   Triggs Raine, Barbara ^b   Flamion, Bruno ^a  

^a UNIVERSITY OF NAMUR   (Belgium)

^b UNIVERSITY OF MANITOBA   (Canada)

^c Halozyme Therapeutics Inc   (United States)

Author keywords

Frontonasal suture; Hemolysis; Hyaluronan; Hyaluronidase; Sinusoidal endothelial cells

Indexed keywords

HYALURONIC ACID; HYALURONIDASE; HYALURONIDASE 2; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONGENITAL BONE DISEASE; CONTROLLED STUDY; DISEASE ASSOCIATION; ENZYME ACTIVITY; HEMATOLOGIC DISEASE; INTRAVASCULAR HEMOLYSIS; LIVER SINUSOID; MALE; MOUSE; MUCOPOLYSACCHARIDOSIS; MUCOPOLYSACCHARIDOSIS IX; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN FOLDING; SKELETON MALFORMATION; THROMBOCYTOPENIA;

ANIMALS; FEMALE; GENOTYPE; HEMATOLOGIC TESTS; HYALURONIC ACID; HYALURONOGLUCOSAMINIDASE; MALE; MICE; MUCOPOLYSACCHARIDOSES; MUSCULOSKELETAL ABNORMALITIES; PHENOTYPE; POLYMERASE CHAIN REACTION; SKULL; THROMBOCYTOPENIA;

MURINAE; MUS; OVIS;

EID: 57349142483     PISSN: 08926638     EISSN: None     Source Type: Journal    
DOI: 10.1096/fj.08-111997     Document Type: Article

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