Bile composition in Alagille Syndrome and PFIC patients having Partial External Biliary Diversion

BMC Gastroenterology

Volumn 8, Issue , 2008, Pages

  Emerick, Karan M ^a,b   Elias, Marc S ^b   Melin Aldana, Hector ^a,b   Strautnieks, Sandra ^c   Thompson, Richard J ^c   Bull, Laura N ^d   Knisely, A S ^e   Whitington, Peter F ^a,b   Green, Richard M ^b  

^a CHILDREN'S MEMORIAL HOSPITAL   (United States)

^b NORTHWESTERN UNIVERSITY   (United States)

^c KING'S COLLEGE LONDON   (United Kingdom)

^d SAN FRANCISCO GENERAL HOSPITAL   (United States)

^e KING S COLLEGE HOSPITAL   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

ALANINE AMINOTRANSFERASE; BILE SALT; BILE SALT EXPORT PROTEIN; BILIRUBIN; CHENODEOXYCHOLIC ACID; CHOLESTEROL; CHOLIC ACID; LIPID; PHOSPHOLIPID; UNCLASSIFIED DRUG; URSODEOXYCHOLIC ACID;

ADOLESCENT; ADULT; ALAGILLE SYNDROME; ALANINE AMINOTRANSFERASE BLOOD LEVEL; ARTICLE; BILE COMPOSITION; BILIARY TRACT SURGERY; BILIRUBIN BLOOD LEVEL; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; DISEASE COURSE; GENE MUTATION; GENOTYPE; HETEROZYGOSITY; HOMOZYGOSITY; HUMAN; HUMAN TISSUE; INTRAHEPATIC CHOLESTASIS; LIVER BIOPSY; PARTIAL EXTERNAL BILIARY DIVERSION; PROGRESSIVE FAMILIAL INTRAHEPATIC CHOLESTASIS; PRURITUS; ABDOMINAL SURGERY; BILE; BIOPSY; GALLBLADDER; GENETICS; INFANT; INTRAHEPATIC BILE DUCT; LIPID METABOLISM; LIVER; METABOLISM; METHODOLOGY; PATHOLOGY; PHYSIOLOGY; PRESCHOOL CHILD; TREATMENT OUTCOME;

ADOLESCENT; ALAGILLE SYNDROME; BILE; BILE DUCTS, INTRAHEPATIC; BIOPSY; CHENODEOXYCHOLIC ACID; CHILD; CHILD, PRESCHOOL; CHOLESTASIS, INTRAHEPATIC; CHOLESTEROL; CHOLIC ACID; DIGESTIVE SYSTEM SURGICAL PROCEDURES; DISEASE PROGRESSION; GALLBLADDER; HUMANS; INFANT; LIPID METABOLISM; LIVER; PHOSPHOLIPIDS; TREATMENT OUTCOME;

EID: 56849131806     PISSN: None     EISSN: 1471230X     Source Type: Journal    
DOI: 10.1186/1471-230X-8-47     Document Type: Article

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