Good response to IL-1β blockade by anakinra in a 23-year-old CINCA/NOMID patient without mutations in the CIAS1 gene. Cytokine profiles and functional studies

Scandinavian Journal of Rheumatology

Volumn 37, Issue 5, 2008, Pages 385-389

  Hedrich, C M ^a   Fiebig, B ^a   Sallmann, S ^a   Bruck, N ^a   Hahn, G ^a   Roesler, J ^a   Roesen Wolff, A ^a   Heubner, G ^b   Gahr, M ^a  

^a UNIVERSITY HOSPITAL CARL GUSTAV CARUS   (Germany)

^b Children's Hospital Freital   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

CYTOKINE; INTERLEUKIN 1BETA; INTERLEUKIN 6; INTERLEUKIN 8; PREDNISOLONE; RECOMBINANT INTERLEUKIN 1 RECEPTOR BLOCKING AGENT; TUMOR NECROSIS FACTOR ALPHA;

ADULT; ARTHROPATHY; ARTICLE; ASEPTIC MENINGITIS; AUTOINFLAMMATORY DISEASE; AUTOSOMAL DOMINANT INHERITANCE; CASE REPORT; CAUCASIAN; CINCA SYNDROME; COGNITION; COLD INDUCED AUTOINFLAMMATORY SYNDROME GENE; CYTOKINE RELEASE; DISEASE ACTIVITY; DRUG DOSE INCREASE; DRUG DOSE REDUCTION; DRUG WITHDRAWAL; FEMALE; GENE; GENE MUTATION; HEADACHE; HUMAN; INFLAMMATION; INTRACRANIAL PRESSURE; KERATOCONJUNCTIVITIS; NUCLEAR MAGNETIC RESONANCE IMAGING; PAPILLEDEMA; PATIENT COMPLIANCE; PERCEPTION DEAFNESS; PRIORITY JOURNAL; PROTEIN CEREBROSPINAL FLUID LEVEL; SKIN MANIFESTATION; SYSTEMIC DISEASE; TREATMENT DURATION; TREATMENT OUTCOME; TREATMENT RESPONSE; URTICARIA; VISUAL IMPAIRMENT;

ADULT; ANTIRHEUMATIC AGENTS; CARRIER PROTEINS; FEMALE; HUMANS; INTERLEUKIN 1 RECEPTOR ANTAGONIST PROTEIN; INTERLEUKIN-1BETA; MUTATION; NERVOUS SYSTEM DISEASES; RHEUMATIC DISEASES; SYNDROME; URTICARIA;

EID: 52949100514     PISSN: 03009742     EISSN: 15027732     Source Type: Journal    
DOI: 10.1080/03009740801978889     Document Type: Article

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