The Leber congenital amaurosis protein AIPL1 functions as part of a chaperone heterocomplex

Investigative Ophthalmology and Visual Science

Volumn 49, Issue 7, 2008, Pages 2878-2887

  Hidalgo de Quintana, Juan ^a   Evans, R Jane ^a   Cheetham, Michael E ^a   Van Der Spuy, Jacqueline ^a  

^a UNIVERSITY COLLEGE LONDON   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

BINDING PROTEIN; CHAPERONE; HEAT SHOCK PROTEIN 70; HEAT SHOCK PROTEIN 90; LEBER CONGENITAL AMAUROSIS PROTEIN AIPL1; NEGATIVE REGULATOR UBIQUITIN PROTEIN 1; TETRATRICOPEPTIDE REPEAT PROTEIN; UNCLASSIFIED DRUG; AIPL1 PROTEIN, HUMAN; BENZOQUINONE DERIVATIVE; CARRIER PROTEIN; GELDANAMYCIN; MACROCYCLIC LACTAM; NUB1 PROTEIN, HUMAN; PEPTIDE FRAGMENT; TRANSCRIPTION FACTOR;

ANIMAL CELL; ARTICLE; BINDING SITE; BIOCHEMISTRY; CONTROLLED STUDY; GENE MUTATION; GENE SEQUENCE; HUMAN; HUMAN CELL; LEBER CONGENITAL AMAUROSIS; NONHUMAN; PHOTORECEPTOR; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN ANALYSIS; PROTEIN BINDING; PROTEIN DOMAIN; PROTEIN FUNCTION; PROTEIN INTERACTION; TWO HYBRID SYSTEM; ANIMAL; CELL STRAIN COS1; CERCOPITHECUS; DRUG ANTAGONISM; GENETICS; LEBER HEREDITARY OPTIC NEUROPATHY; METABOLISM; MUTATION; PATHOLOGY; PROTEIN TERTIARY STRUCTURE; RETINA TUMOR; RETINOBLASTOMA; TUMOR CELL LINE;

ANIMALS; BENZOQUINONES; CARRIER PROTEINS; CELL LINE, TUMOR; CERCOPITHECUS AETHIOPS; COS CELLS; HSP70 HEAT-SHOCK PROTEINS; HSP90 HEAT-SHOCK PROTEINS; HUMANS; LACTAMS, MACROCYCLIC; MOLECULAR CHAPERONES; MUTATION; OPTIC ATROPHY, HEREDITARY, LEBER; PEPTIDE FRAGMENTS; PROTEIN STRUCTURE, TERTIARY; RETINAL NEOPLASMS; RETINOBLASTOMA; TRANSCRIPTION FACTORS; TWO-HYBRID SYSTEM TECHNIQUES;

EID: 48249119911     PISSN: 01460404     EISSN: 15525783     Source Type: Journal    
DOI: 10.1167/iovs.07-1576     Document Type: Article

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