Changes in the amounts of myelin lipids and molecular species of plasmalogen PE in the brain of an autopsy case with d-bifunctional protein deficiency

Neuroscience Letters

Volumn 442, Issue 1, 2008, Pages 4-9

  Saitoh, Makiko ^a   Yamashita, Sumimasa ^b   Shimozawa, Nobuyuki ^c   Mizuguchi, Masashi ^a   Iwamori, Masao ^d  

^a UNIVERSITY OF TOKYO   (Japan)

^b Kanagawa Prefectural Medical Center for Children   (Japan)

^c GIFU UNIVERSITY   (Japan)

^d KINKI UNIVERSITY   (Japan)

Author keywords

d Bifunctional protein; Gangliosides; Myelin lipids; Peroxisome; Plasmalogen type phosphatidylethanolamine; Polyunsaturated fatty acids

Indexed keywords

GALACTOSYLCERAMIDE; GANGLIOSIDE; PHOSPHATIDYLETHANOLAMINE; PHOSPHOLIPID; PLASMALOGEN; POLYUNSATURATED FATTY ACID; SULFATIDE;

ANAMNESIS; ARTICLE; AUTOPSY; BRAIN TISSUE; CASE REPORT; CHILD; CLINICAL FEATURE; FEMALE; GENETIC ANALYSIS; GRAY MATTER; HUMAN; HUMAN TISSUE; INFANT; LIPID BRAIN LEVEL; MALE; NUCLEAR MAGNETIC RESONANCE IMAGING; OXIDATIVE STRESS; PRIORITY JOURNAL; PROTEIN DEFICIENCY; WHITE MATTER;

3-HYDROXYACYL COA DEHYDROGENASES; AUTOPSY; BRAIN CHEMISTRY; BRAIN DISEASES; BRAIN DISEASES, METABOLIC, INBORN; CHROMATOGRAPHY, THIN LAYER; ENOYL-COA HYDRATASE; HUMANS; INFANT, NEWBORN; ISOMERASES; MALE; MULTIENZYME COMPLEXES; MYELIN SHEATH; PHOSPHOLIPIDS; PLASMALOGENS;

EID: 47749141451     PISSN: 03043940     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.neulet.2008.06.071     Document Type: Article

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