Establishment of a cell model of ALS disease: Golgi apparatus disruption occurs independently from apoptosis

Biotechnology Letters

Volumn 30, Issue 4, 2008, Pages 603-610

  Gomes, Catarina ^a   Palma, Angelina S ^a   Almeida, Rui ^a   Regalla, Manuela ^a   McCluskey, Leo F ^b   Trojanowski, John Q ^b   Costa, Júlia ^a,c  

^a INSTITUTO DE TECNOLOGIA QUÍMICA E BIOLÓGICA   (Portugal)

^b UNIVERSITY OF PENNSYLVANIA   (United States)

^c INSTITUTO DE BIOLOGIA EXPERIMENTAL E TECNOLÓGICA   (Portugal)

Author keywords

Amyotrophic lateral sclerosis; Apoptosis; Golgi apparatus; Human SOD1 mutant; NSC 34 motor neuron cell line

Indexed keywords

CELL PROLIFERATION; DISEASES; ENZYME ACTIVITY; MEDICAL PROBLEMS; MUTAGENESIS;

AMYOTROPHIC LATERAL SCLEROSIS; GOLGI APPARATUS (GA); HUMAN SOD1 MUTANT; NSC-34 MOTOR NEURON CELL LINE; SPINAL CORDS;

CELL DEATH;

CASPASE 3; COPPER ZINC SUPEROXIDE DISMUTASE; SUPEROXIDE DISMUTASE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL; APOPTOSIS; ARTICLE; CELL LINE; CELL SURVIVAL; FLOW CYTOMETRY; FLUORESCENCE MICROSCOPY; GENETICS; GOLGI COMPLEX; HUMAN; METABOLISM; MITOCHONDRIAL MEMBRANE POTENTIAL; MOTONEURON; MOUSE; MUTATION; PATHOLOGY;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; APOPTOSIS; CASPASE 3; CELL LINE; CELL SURVIVAL; FLOW CYTOMETRY; GOLGI APPARATUS; HUMANS; MEMBRANE POTENTIAL, MITOCHONDRIAL; MICE; MICROSCOPY, FLUORESCENCE; MOTOR NEURONS; MUTATION; SUPEROXIDE DISMUTASE;

EID: 43149109289     PISSN: 01415492     EISSN: 15736776     Source Type: Journal    
DOI: 10.1007/s10529-007-9595-z     Document Type: Article

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