Hematopoietic cell transplantation ameliorates clinical phenotype and progression of the CNS pathology in the mouse model of late onset Krabbe disease

Journal of Neuropathology and Experimental Neurology

Volumn 64, Issue 7, 2005, Pages 565-575

  Yagi, Takashi ^a   Matsuda, Junko ^a,b   Tominaga, Kumiko ^b   Suzuki, Kunihiko ^a,c   Suzuki, Kinuko ^a  

^a UNIVERSITY OF NORTH CAROLINA SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF TOKUSHIMA   (Japan)

^c TOKAI UNIVERSITY   (Japan)

Author keywords

Demyelination; Globoid cell leukodystrophy; Green fluorescence protein; Hypertrophic neuropathy; Remyelination; Twitcher mouse

Indexed keywords

GALACTOSYLCERAMIDASE; GREEN FLUORESCENT PROTEIN; SAPOSIN A; SPHINGOLIPID ACTIVATOR PROTEIN; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BONE MARROW TRANSPLANTATION; CELL INFILTRATION; CENTRAL NERVOUS SYSTEM DISEASE; CHIMERA; CLINICAL FEATURE; CONTROLLED STUDY; DEMYELINATING DISEASE; DEMYELINATION; DISEASE COURSE; DISEASE SEVERITY; ENZYME ACTIVITY; GLOBOID CELL LEUKODYSTROPHY; HEMATOPOIETIC STEM CELL TRANSPLANTATION; INFLAMMATION; MACROPHAGE; MOUSE; NEUROPATHY; NONHUMAN; ONSET AGE; PERINATAL PERIOD; PERIPHERAL NERVE; PHENOTYPE; PRIORITY JOURNAL; SYMPTOMATOLOGY; TRANSGENIC MOUSE;

EID: 22244445463     PISSN: 00223069     EISSN: None     Source Type: Journal    
DOI: 10.1097/01.jnen.0000171646.01966.0c     Document Type: Article

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