Development of sensory, motor and behavioral deficits in the murine model of Sanfilippo Syndrome type B

PLoS ONE

Volumn 2, Issue 8, 2007, Pages

  Heldermon, Coy D ^a   Hennig, Anne K ^a   Ohlemiller, Kevin K ^a   Ogilvie, Judith M ^b   Herzog, Erik D ^a   Breidenbach, Annalisa ^a   Vogler, Carole ^c   Wozniak, David F ^d   Sands, Mark S ^a  

^a WASHINGTON UNIVERSITY   (United States)

^b SAINT LOUIS UNIVERSITY   (United States)

^c SAINT LOUIS UNIVERSITY SCHOOL OF MEDICINE   (United States)

^d WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; B WAVE; C57BL 6 MOUSE; CELL COUNT; CIRCADIAN RHYTHM; CONTROLLED STUDY; COORDINATION DISORDER; DISEASE COURSE; ELECTRORETINOGRAPHY; EVOKED BRAIN STEM AUDITORY RESPONSE; HAIR CELL; HEARING LOSS; HISTOPATHOLOGY; INNER EAR; LOCOMOTION; MIDDLE EAR; MOTOR PERFORMANCE; MOUSE; NONHUMAN; PHENOTYPIC VARIATION; PIGMENT EPITHELIUM; PURKINJE CELL; ROTAROD TEST; SANFILIPPO SYNDROME; SUPRACHIASMATIC NUCLEUS; WILD TYPE;

ACETYLGLUCOSAMINIDASE; ANIMALS; BEHAVIOR, ANIMAL; CEREBELLUM; CHILD; CIRCADIAN RHYTHM; DISEASE MODELS, ANIMAL; EAR, INNER; EAR, MIDDLE; ELECTRORETINOGRAPHY; EVOKED POTENTIALS, AUDITORY; FEMALE; HEARING; HUMANS; LYSOSOMES; MALE; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; MOTOR ACTIVITY; MUCOPOLYSACCHARIDOSIS III; PHENOTYPE; RETINA; ROTAROD PERFORMANCE TEST; SUPRACHIASMATIC NUCLEUS; VISION, OCULAR;

ANIMALIA; MURINAE; MUS;

EID: 40749147092     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0000772     Document Type: Article

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