RBP4 Disrupts Vitamin A Uptake Homeostasis in a STRA6-Deficient Animal Model for Matthew-Wood Syndrome

Cell Metabolism

Volumn 7, Issue 3, 2008, Pages 258-268

  Isken, Andrea ^a   Golczak, Marcin ^b   Oberhauser, Vitus ^a   Hunzelmann, Silke ^a,b   Driever, Wolfgang ^a   Imanishi, Yoshikazu ^b   Palczewski, Krzysztof ^b   von Lintig, Johannes ^a,b  

^a UNIVERSITY OF FREIBURG   (Germany)

^b CASE WESTERN RESERVE UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

HUMDISEASE

Indexed keywords

MEMBRANE PROTEIN; MORPHOLINO OLIGONUCLEOTIDE; OLIGONUCLEOTIDE; PHOSPHATIDYLCHOLINE; PROTEIN STRA6; RETINOIC ACID RECEPTOR; RETINOL; RETINOL ACYLTRANSFERASE; RETINOL BINDING PROTEIN; RETINOL BINDING PROTEIN 4; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL STRAIN 3T3; CONGENITAL HEART MALFORMATION; CONTROLLED STUDY; CRANIOFACIAL MALFORMATION; EMBRYO; EMBRYONAL TISSUE; EMBRYOPATHY; EYE DEVELOPMENT; GENETIC REGULATION; HUMAN; HUMAN CELL; MALFORMATION SYNDROME; MATTHEW WOOD SYNDROME; METABOLIC BALANCE; MICROPHTHALMIA; NONHUMAN; NUCLEOTIDE SEQUENCE; PRIORITY JOURNAL; PROTEIN DEFICIENCY; PROTEIN FUNCTION; PROTEIN TRANSPORT; SIGNAL TRANSDUCTION; VITAMIN METABOLISM; ZEBRA FISH;

ABNORMALITIES, MULTIPLE; ACYLTRANSFERASES; ANIMALS; CARDIOVASCULAR ABNORMALITIES; CRANIOFACIAL ABNORMALITIES; DISEASE MODELS, ANIMAL; EYE; GENE DELETION; GENE EXPRESSION REGULATION, DEVELOPMENTAL; HOMEOSTASIS; HUMANS; MEMBRANE PROTEINS; MICE; MORPHOLINES; NIH 3T3 CELLS; OLIGONUCLEOTIDES, ANTISENSE; RETINOL-BINDING PROTEINS, PLASMA; SYNDROME; TIME FACTORS; TRANSDUCTION, GENETIC; TRETINOIN; VITAMIN A; ZEBRAFISH; ZEBRAFISH PROTEINS;

ANIMALIA; DANIO RERIO;

EID: 39649089801     PISSN: 15504131     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.cmet.2008.01.009     Document Type: Article

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