Poison and antidote: A novel model to study pathogenesis and therapy of LHON

Annals of Neurology

Volumn 56, Issue 2, 2004, Pages 171-172

  Manfredi, Giovanni ^a   Beal, M Flint ^a  

^a WEILL CORNELL MEDICAL COLLEGE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ANTIOXIDANT; MITOCHONDRIAL DNA; NEUROTOXIN; PARVOVIRUS VECTOR; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE); RIBOZYME; ROTENONE;

ANIMAL MODEL; EDITORIAL; GENE; GENE EXPRESSION; GENE MUTATION; GENE OVEREXPRESSION; HUMAN; KNOCKOUT MOUSE; LEBER HEREDITARY OPTIC NEUROPATHY; MITOCHONDRIAL DNA DISORDER; MITOCHONDRIAL RESPIRATION; MOLECULAR MECHANICS; NDUFA1 GENE; OPTIC NERVE DISEASE; PATHOGENESIS; PHENOTYPE; PRIORITY JOURNAL; RESPIRATORY CHAIN; RETINA DEGENERATION; SOD2 GENE;

ANIMALS; DISEASE MODELS, ANIMAL; GENE THERAPY; HUMANS; MEMBRANE PROTEINS; MICE; NADH DEHYDROGENASE; OPTIC ATROPHY, HEREDITARY, LEBER; SUPEROXIDE DISMUTASE;

EID: 3843123186     PISSN: 03645134     EISSN: None     Source Type: Journal    
DOI: 10.1002/ana.20243     Document Type: Editorial

References (10)

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