Spinal and bulbar muscular atrophy: Skeletal muscle pathology in male patients and heterozygous females

Journal of the Neurological Sciences

Volumn 264, Issue 1-2, 2008, Pages 100-105

  Sorarù, Gianni ^a   D'Ascenzo, Carla ^a   Polo, Alberto ^b   Palmieri, Arianna ^a   Baggio, Linda ^a   Vergani, Lodovica ^a   Gellera, Cinzia ^c   Moretto, Giuseppe ^d   Pegoraro, Elena ^a   Angelini, Corrado ^a  

^a UNIVERSITY OF PADOVA   (Italy)

^b UNIVERSITY OF MILAN   (Italy)

^c DEPARTMENT OF NEUROSURGERY   (Italy)

^d BORGO TRENTO HOSPITAL   (Italy)

Author keywords

Denervation; Myogenic changes; Satellite cells; SBMA; Skeletal muscle

Indexed keywords

ADULT; AGED; ARTICLE; BULBAR PARALYSIS; CLINICAL ARTICLE; CORRELATION ANALYSIS; DENERVATION; DISABILITY; DISEASE DURATION; FEMALE; HEREDITARY MOTOR SENSORY NEUROPATHY; HETEROZYGOSITY; HUMAN; HUMAN TISSUE; MALE; MUSCLE BIOPSY; MUSCLE INJURY; MYOPATHY; PATHOGENESIS; PATHOLOGY; PRIORITY JOURNAL; SATELLITE CELL; SKELETAL MUSCLE; SPINAL MUSCULAR ATROPHY;

ADULT; AGED; AGED, 80 AND OVER; BIOPSY; CREATINE KINASE; DISEASE PROGRESSION; DNA REPEAT EXPANSION; FEMALE; GENETIC PREDISPOSITION TO DISEASE; HETEROZYGOTE; HUMANS; MALE; MIDDLE AGED; MOTOR NEURONS; MUSCLE FIBERS; MUSCLE, SKELETAL; MUSCULAR ATROPHY, SPINAL; NERVE DEGENERATION; PEPTIDES; RECEPTORS, ANDROGEN; SATELLITE CELLS, SKELETAL MUSCLE; SEVERITY OF ILLNESS INDEX; SEX CHARACTERISTICS;

EID: 36549087642     PISSN: 0022510X     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.jns.2007.08.012     Document Type: Article

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