Characterization of hepatic and brain metabolism in young adults with glycogen storage disease type 1: A magnetic resonance spectroscopy study

American Journal of Physiology - Endocrinology and Metabolism

Volumn 293, Issue 5, 2007, Pages

  Weghuber, D ^a,c   Mandl, M ^a   Krssak M ^a   Roden, M ^b   Nowotny, P ^a   Brehm, A ^a   Krebs, M ^a   Widhalm, K ^a   Bischof, M G ^a  

^a MEDICAL UNIVERSITY OF VIENNA   (Austria)

^b HANUSCH HOSPITAL   (Austria)

^c Paracelsus Private Medical School   (Austria)

Author keywords

Endogenous glucose production; Glucose 6 phospate; Hypoglycemia; Intrahepatocellular lipid content

Indexed keywords

CREATINE; GLUCAGON; GLUCOSE; GLYCOGEN; LACTIC ACID; LIPID; ORGANOPHOSPHATE; PHOSPHATE;

ADULT; ARTICLE; BIOACCUMULATION; BLOOD BRAIN BARRIER; BODY MASS; BRAIN METABOLISM; CARBON NUCLEAR MAGNETIC RESONANCE; CASE REPORT; COMPARATIVE STUDY; DISEASE SEVERITY; FEMALE; GLUCONEOGENESIS; GLUCOSE BRAIN LEVEL; GLUCOSE METABOLISM; GLYCOGEN LIVER LEVEL; GLYCOGEN STORAGE DISEASE TYPE 1; HUMAN; HYPOGLYCEMIA; LIPID LIVER LEVEL; LIVER LEVEL; LIVER METABOLISM; MALE; NUCLEAR MAGNETIC RESONANCE SPECTROSCOPY; PHOSPHORUS NUCLEAR MAGNETIC RESONANCE; PRIORITY JOURNAL; PROTON NUCLEAR MAGNETIC RESONANCE; SYMPTOM; UPREGULATION;

ADULT; BLOOD GLUCOSE; BRAIN; BUTYRATES; C-REACTIVE PROTEIN; FATTY ACIDS, NONESTERIFIED; FEMALE; GLUCOSE; GLYCOGEN; GLYCOGEN STORAGE DISEASE TYPE I; HUMANS; INSULIN; LACTATES; LIVER; MAGNETIC RESONANCE SPECTROSCOPY; MALE; PHOSPHATES;

EID: 36148980050     PISSN: 01931849     EISSN: 15221555     Source Type: Journal    
DOI: 10.1152/ajpendo.00658.2006     Document Type: Article

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