Marfan-like skeletal phenotype in the tight skin (Tsk) mouse

Calcified Tissue International

Volumn 81, Issue 4, 2007, Pages 305-315

  Barisic Dujmovic, Tatjana ^a   Boban, Ivana ^a   Adams, Douglas J ^a   Clark, Stephen H ^a  

^a UNIVERSITY OF CONNECTICUT HEALTH CENTER   (United States)

Author keywords

Fibrillin 1; Marfan syndrome; Microfibril; Osteopenia; Tight skin mutation

Indexed keywords

FIBRILLIN 1;

ANIMAL CELL; ANIMAL TISSUE; ARTICLE; BONE CELL; BONE DENSITY; BONE DEVELOPMENT; BONE MARROW; BONE METABOLISM; CELL CULTURE; CONTROLLED STUDY; CORTICAL BONE; EXTRACELLULAR MATRIX; FEMUR; GENE EXPRESSION; GENE MUTATION; MARFAN SYNDROME; MOUSE; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; PROTEIN FUNCTION; STROMA CELL; TRABECULAR BONE; TRANSGENIC MOUSE; VERTEBRA;

ALKALINE PHOSPHATASE; ANIMALS; BONE AND BONES; BONE DENSITY; BONE MARROW CELLS; CELL DIFFERENTIATION; CELLS, CULTURED; CHROMOSOMES, MAMMALIAN; COLLAGEN TYPE I; CROSSES, GENETIC; DISEASE MODELS, ANIMAL; FEMALE; FEMUR; GENE DUPLICATION; HISTOCYTOCHEMISTRY; MALE; MARFAN SYNDROME; MICE; MICE, INBRED C57BL; MICE, MUTANT STRAINS; MICROFILAMENT PROTEINS; MUTATION; OSTEOBLASTS; OSTEOCALCIN; PHENOTYPE; RNA, MESSENGER; SIALOGLYCOPROTEINS; SKIN ABNORMALITIES; STROMAL CELLS; TIBIA; TIME FACTORS; TOMOGRAPHY, X-RAY COMPUTED;

EID: 34848881653     PISSN: 0171967X     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00223-007-9059-4     Document Type: Article

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