Functional rescue of elastin insufficiency in mice by the human elastin gene: Implications for mouse models of human disease

Circulation Research

Volumn 101, Issue 5, 2007, Pages 523-531

  Hirano, Eiichi ^a   Knutsen, Russell H ^a   Sugitani, Hideki ^a   Ciliberto, Christopher H ^a   Mecham, Robert P ^a  

^a WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

Elastin; Supravalvular aortic stenosis; Transgenic mice; Vascular disease

Indexed keywords

ELASTIN;

ALTERNATIVE RNA SPLICING; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BACTERIAL ARTIFICIAL CHROMOSOME; CARDIOVASCULAR DISEASE; CONTROLLED STUDY; ELASTIC FIBER; FEMALE; GENE CONTROL; GENE EXPRESSION; HYPERTENSION; LETHALITY; MOUSE; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; PROTEIN PROTEIN INTERACTION; TRANSGENE; VASCULAR DISEASE;

ALTERNATIVE SPLICING; ANIMALS; AORTA; AORTIC STENOSIS, SUBVALVULAR; CHROMOSOMES, ARTIFICIAL, BACTERIAL; CUTIS LAXA; DISEASE MODELS, ANIMAL; DNA; ELASTIN; FEMALE; GENE EXPRESSION REGULATION; HUMANS; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; PHENOTYPE;

EID: 34548304825     PISSN: 00097330     EISSN: None     Source Type: Journal    
DOI: 10.1161/CIRCRESAHA.107.153510     Document Type: Article

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