Usherin is required for maintenance of retinal photoreceptors and normal development of cochlear hair cells

Proceedings of the National Academy of Sciences of the United States of America

Volumn 104, Issue 11, 2007, Pages 4413-4418

  Liu, Xiaoqing ^a   Bulgakov, Oleg V ^a   Darrow, Keith N ^a   Pawlyk, Basil ^a   Adamian, Michael ^a   Liberman, M Charles ^a   Li, Tiansen ^a  

^a MASSACHUSETTS EYE AND EAR INFIRMARY   (United States)

Author keywords

Photoreceptor degeneration; Retina; Retinitis pigmentosa

Indexed keywords

SCLEROPROTEIN; UNCLASSIFIED DRUG; USHERIN; USH2A PROTEIN, HUMAN; USH2A PROTEIN, MOUSE;

AMPHIBIA; ANIMAL CELL; ANIMAL TISSUE; ARTICLE; CARBOXY TERMINAL SEQUENCE; CELL MEMBRANE; COCHLEA; CONGENITAL DEAFNESS; CONTROLLED STUDY; EXTRACELLULAR MATRIX; GENE; GENE DISRUPTION; GENE TARGETING; HAIR CELL; MAMMAL; MOUSE; NONHUMAN; NUCLEOTIDE SEQUENCE; PHOTORECEPTOR; POSTNATAL DEVELOPMENT; PRIORITY JOURNAL; PROTEIN DOMAIN; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; RETINA DEGENERATION; SIGNAL TRANSDUCTION; USH2A GENE; USHER SYNDROME; VISUAL DISORDER; ANIMAL; C57BL MOUSE; CONFOCAL MICROSCOPY; GENE EXPRESSION REGULATION; GROWTH, DEVELOPMENT AND AGING; HUMAN; METABOLISM; MOLECULAR GENETICS; MOUSE MUTANT; PATHOLOGY; PHYSIOLOGY; RETINA; RETINITIS PIGMENTOSA; TRANSGENIC MOUSE;

AMPHIBIA; MAMMALIA; MUS;

ANIMALS; COCHLEA; EXTRACELLULAR MATRIX PROTEINS; GENE EXPRESSION REGULATION, DEVELOPMENTAL; HAIR CELLS; HUMANS; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; MICE, TRANSGENIC; MICROSCOPY, CONFOCAL; MOLECULAR SEQUENCE DATA; RETINA; RETINITIS PIGMENTOSA;

EID: 34248353947     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.0610950104     Document Type: Article

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