The mannan-binding lectin pathway and lung disease in cystic fibrosis-dysfunction of mannan-binding lectin-associated serine protease 2 (MASP-2) may be a major modifier

Clinical Immunology

Volumn 121, Issue 3, 2006, Pages 324-331

  Olesen, H V ^a   Jensenius, J C ^b   Steffensen, R ^c   Thiel, S ^b   Schiotz P O ^a  

^a AARHUS UNIVERSITY HOSPITAL   (Denmark)

^b AARHUS UNIVERSITY   (Denmark)

^c AALBORG UNIVERSITY HOSPITAL   (Denmark)

Author keywords

Complement activation; Cystic fibrosis; Mannan binding lectin; MBL associated serine proteases; Modifier genes; Spirometry

Indexed keywords

MANNAN BINDING LECTIN; MANNAN BINDING LECTIN ASSOCIATED SERINE PROTEASE 2; SERINE PROTEINASE; UNCLASSIFIED DRUG;

ADOLESCENT; ADULT; ARTICLE; CHILD; CONCENTRATION (PARAMETERS); CONTROLLED STUDY; CYSTIC FIBROSIS; DISEASE COURSE; DISEASE SEVERITY; FEMALE; GENE MUTATION; GENOTYPE; HETEROZYGOSITY; HUMAN; LUNG DISEASE; LUNG FUNCTION; LUNG INFECTION; MAJOR CLINICAL STUDY; MALE; PRIORITY JOURNAL; PROTEIN DEFICIENCY; RISK FACTOR; SIGNAL TRANSDUCTION;

ADOLESCENT; ADULT; CHILD; CHILD, PRESCHOOL; CYSTIC FIBROSIS; FEMALE; GENOTYPE; HUMANS; LUNG; MALE; MANNOSE-BINDING LECTIN; MANNOSE-BINDING PROTEIN-ASSOCIATED SERINE PROTEASES;

EID: 33750940959     PISSN: 15216616     EISSN: 15217035     Source Type: Journal    
DOI: 10.1016/j.clim.2006.08.014     Document Type: Article

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