Premature proliferative arrest of cricopharyngeal myoblasts in oculo-pharyngeal muscular dystrophy: Therapeutic perspectives of autologous myoblast transplantation

Neuromuscular Disorders

Volumn 16, Issue 11, 2006, Pages 770-781

  Périé, Sophie ^a,b   Mamchaoui, Kamel ^a   Mouly, Vincent ^a   Blot, Stéphane ^c   Bouazza, Belaïd ^a   Thornell, Lars Eric ^d   St Guily, Jean Lacau ^b   Butler Browne, Gillian ^a  

^a PITIÉ SALPÊTRIÈRE HOSPITAL   (France)

^b SORBONNE UNIVERSITÉ   (France)

^c ECOLE NATIONALE VÉTÉRINAIRE D ALFORT   (France)

^d Center for Musculoskeletal Research   (Sweden)

Author keywords

Autograft of myoblasts; Myogenicity; Oculo pharyngeal muscular dystrophy; Poly(A) binding protein nuclear 1; Satellite cells cultures; Senescence

Indexed keywords

BROXURIDINE; POLY A BINDING PROTEIN NUCLEAR 1; PROTEIN; UNCLASSIFIED DRUG;

ADULT; AGED; ARTICLE; AUTOGRAFT; AUTOTRANSPLANTATION; CELL AGING; CELL CULTURE; CELL PROLIFERATION; CELL TRANSPLANTATION; CLINICAL ARTICLE; CONTROLLED STUDY; CYTOPLASM; HUMAN; HUMAN TISSUE; LIFESPAN; MUSCLE FIBER CULTURE; MUSCLE FUNCTION; MUTATION; MYOBLAST; OCULOPHARYNGEAL MUSCULAR DYSTROPHY; PHENOTYPE; PRIORITY JOURNAL; SATELLITE CELL; SKELETAL MUSCLE;

EID: 33750440221     PISSN: 09608966     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.nmd.2006.07.022     Document Type: Article

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