Deafness in LIMP2-deficient mice due to early loss of the potassium channel KCNQ1/KCNE1 in marginal cells of the stria vascularis

Journal of Physiology

Volumn 576, Issue 1, 2006, Pages 73-86

  Knipper, Marlies ^a   Claussen, Cathrin ^b   Rüttiger, Lukas ^a   Zimmermann, Ulrike ^a   Lüllmann Rauch, Renate ^b   Eskelinen, Eeva Liisa ^c   Schröder, Jenny ^b   Schwake, Michael ^b   Saftig, Paul ^b  

^a UNIVERSITY HOSPITAL TÜBINGEN   (Germany)

^b UNIVERSITY OF KIEL   (Germany)

^c UNIVERSITY OF HELSINKI   (Finland)

Author keywords

[No Author keywords available]

Indexed keywords

LYSOSOMAL MEMBRANE PROTEIN 2; MEGALIN; MEMBRANE PROTEIN; POTASSIUM CHANNEL; POTASSIUM CHANNEL KCNE1; POTASSIUM CHANNEL KCNQ1; UNCLASSIFIED DRUG; CELL PROTEIN; ION CHANNEL; PROTEIN LIMP2;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BETA CHAIN; COCHLEA; CONTROLLED STUDY; CORRELATION ANALYSIS; CORTI ORGAN; ENDOCYTOSIS; FLUORESCENCE ANALYSIS; HEARING LOSS; IMMUNOHISTOCHEMISTRY; LYSOSOME MEMBRANE; MEMBRANE TRANSPORT; MOUSE; NONHUMAN; OTOACOUSTIC EMISSION; PRIORITY JOURNAL; PROTEIN DEFICIENCY; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN LOCALIZATION; STRIA VASCULARIS; VESTIBULAR SYSTEM; ANIMAL TISSUE; AUDITORY THRESHOLD; COCHLEAR NERVE; HEARING IMPAIRMENT; PROTEIN DEPLETION; SENSITIVITY ANALYSIS; SPIRAL GANGLION; SURFACE PROPERTY;

EID: 33748909207     PISSN: 00223751     EISSN: 14697793     Source Type: Journal    
DOI: 10.1113/jphysiol.2006.116889     Document Type: Article

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