A zebrafish model of human barth syndrome reveals the essential role of tafazzin in cardiac development and function

Circulation Research

Volumn 99, Issue 2, 2006, Pages 201-208

  Khuchua, Zaza ^a   Yue, Zou ^a   Batts, Lorene ^a   Strauss, Arnold W ^a  

^a MONROE CARELL JR CHILDREN S HOSPITAL AT VANDERBILT   (United States)

Author keywords

Barth syndrome; Cardiac development; Cardiomyopathy; Membrane lipids; Tafazzin; Zebrafish

Indexed keywords

ACYLTRANSFERASE; CARDIOLIPIN; MESSENGER RNA; PROTEIN; TAFAZZIN; UNCLASSIFIED DRUG; COMPLEMENTARY RNA; TAFAZZIN PROTEIN, ZEBRAFISH; TRANSCRIPTION FACTOR; ZEBRAFISH PROTEIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BARTH SYNDROME; BRADYCARDIA; CONTROLLED STUDY; DISEASE SEVERITY; EMBRYO; EYE DEVELOPMENT; FERTILIZATION; GENERALIZED EDEMA; HEART DEVELOPMENT; HEART FAILURE; HEART FUNCTION; NONHUMAN; PERICARDIAL EFFUSION; PHENOTYPE; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN FUNCTION; ZEBRA FISH; ANIMAL; CHILD DEVELOPMENT; CONGESTIVE CARDIOMYOPATHY; DISEASE MODEL; DRUG ANTAGONISM; GENE EXPRESSION REGULATION; GENETICS; GROWTH, DEVELOPMENT AND AGING; HEART; HUMAN; INFANT; PHYSIOLOGY; SYNDROME;

ANIMALS; CARDIOMYOPATHY, DILATED; CHILD DEVELOPMENT; DISEASE MODELS, ANIMAL; GENE EXPRESSION REGULATION, DEVELOPMENTAL; HEART; HUMANS; INFANT; RNA, ANTISENSE; RNA, MESSENGER; SYNDROME; TRANSCRIPTION FACTORS; ZEBRAFISH; ZEBRAFISH PROTEINS;

EID: 33747593581     PISSN: 00097330     EISSN: None     Source Type: Journal    
DOI: 10.1161/01.RES.0000233378.95325.ce     Document Type: Article

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