-
1
-
-
0028309683
-
Human airway ion transport
-
Boucher RC. Human airway ion transport. Am J Respir Crit Care Med 1994;150:271-281; 581-593.
-
(1994)
Am J Respir Crit Care Med
, vol.150
, pp. 271-281
-
-
Boucher, R.C.1
-
2
-
-
0032956071
-
CFTR is a conductance regulator as well as a chloride channel
-
Schwiebert EM, Benos DJ, Egan ME, Stutts MJ, Guggino WB. CFTR is a conductance regulator as well as a chloride channel. Physiol Rev 1999;79:S145-S166.
-
(1999)
Physiol Rev
, vol.79
-
-
Schwiebert, E.M.1
Benos, D.J.2
Egan, M.E.3
Stutts, M.J.4
Guggino, W.B.5
-
3
-
-
0032616420
-
The CFTR and its function in epithelial transport
-
Kunzelmann K. The CFTR and its function in epithelial transport. Rev Physiol Biochem Pharmacol 1999;137:1-70.
-
(1999)
Rev Physiol Biochem Pharmacol
, vol.137
, pp. 1-70
-
-
Kunzelmann, K.1
-
4
-
-
0030970422
-
Cystic fibrosis transmembrane conductance regulator inverts protein kinase A-mediated regulation of epithelial sodium channel single channel kinetics
-
Stutts MJ, Rossier BC, Boucher RC. Cystic fibrosis transmembrane conductance regulator inverts protein kinase A-mediated regulation of epithelial sodium channel single channel kinetics. J Biol Chem 1997;272:14037-14040.
-
(1997)
J Biol Chem
, vol.272
, pp. 14037-14040
-
-
Stutts, M.J.1
Rossier, B.C.2
Boucher, R.C.3
-
5
-
-
0346505482
-
New concepts of the pathogenesis of cystic fibrosis lung disease
-
Boucher RC. New concepts of the pathogenesis of cystic fibrosis lung disease. Eur J Respir 2004;23:146-158.
-
(2004)
Eur J Respir
, vol.23
, pp. 146-158
-
-
Boucher, R.C.1
-
6
-
-
0037027912
-
An overview of the pathogenesis of cystic fibrosis lung disease
-
Boucher RC. An overview of the pathogenesis of cystic fibrosis lung disease. Adv Drug Deliv Rev 2002;54:1359-1371.
-
(2002)
Adv Drug Deliv Rev
, vol.54
, pp. 1359-1371
-
-
Boucher, R.C.1
-
7
-
-
0032530370
-
Coordinated clearance of periciliary liquid and mucus from airway surfaces
-
Matsui H, Randell SH, Peretti SW, Davis W, Boucher RC. Coordinated clearance of periciliary liquid and mucus from airway surfaces. J Clin Invest 1998;102:1125-1131.
-
(1998)
J Clin Invest
, vol.102
, pp. 1125-1131
-
-
Matsui, H.1
Randell, S.H.2
Peretti, S.W.3
Davis, W.4
Boucher, R.C.5
-
9
-
-
0031862237
-
Number and proliferation of basal and parabasal cells in normal human airway epithelium
-
Boers JE, Ambergen AW, Thunnissen FBJM. Number and proliferation of basal and parabasal cells in normal human airway epithelium. Am J Respir Crit Care Med 1998;157:2000-2006.
-
(1998)
Am J Respir Crit Care Med
, vol.157
, pp. 2000-2006
-
-
Boers, J.E.1
Ambergen, A.W.2
Thunnissen, F.B.J.M.3
-
10
-
-
0014353749
-
Pulmonary changes and cor pulmonale in mucoviscidosis
-
Wentworth P, Gough J, Wentworth JE. Pulmonary changes and cor pulmonale in mucoviscidosis. Thorax 1968;23:582-589.
-
(1968)
Thorax
, vol.23
, pp. 582-589
-
-
Wentworth, P.1
Gough, J.2
Wentworth, J.E.3
-
11
-
-
30344450116
-
High-resolution computed tomography imaging of airway disease in infants with cystic fibrosis
-
Martinez TM, Llapur CJ, Williams TH, Coates C, Gunderman R, Cohen MD, Howenstine MS, Saba O, Coxson HO, Tepper RS. High-resolution computed tomography imaging of airway disease in infants with cystic fibrosis. Am J Respir Crit Care Med 2005;172:1133-1138.
-
(2005)
Am J Respir Crit Care Med
, vol.172
, pp. 1133-1138
-
-
Martinez, T.M.1
Llapur, C.J.2
Williams, T.H.3
Coates, C.4
Gunderman, R.5
Cohen, M.D.6
Howenstine, M.S.7
Saba, O.8
Coxson, H.O.9
Tepper, R.S.10
-
13
-
-
1542287428
-
Structural airway abnormalities in infants and young children with cystic fibrosis
-
Long FR, Roger S, Williams BS, Castile RG. Structural airway abnormalities in infants and young children with cystic fibrosis. J Pediatr 2004;144:154-161.
-
(2004)
J Pediatr
, vol.144
, pp. 154-161
-
-
Long, F.R.1
Roger, S.2
Williams, B.S.3
Castile, R.G.4
-
14
-
-
0022462591
-
Quantitative aspects of lung pathology in cystic fibrosis
-
Sobonya RE, Taussig LM. Quantitative aspects of lung pathology in cystic fibrosis. Am Rev Respir Dis 1986;134:290-295.
-
(1986)
Am Rev Respir Dis
, vol.134
, pp. 290-295
-
-
Sobonya, R.E.1
Taussig, L.M.2
-
15
-
-
0037090744
-
Clinical findings and lung pathology in children with cystic fibrosis
-
Hamutcu R, Rowland JM, Horn MV, Kaminsky C, MacLaughlin EF, Starnes VA, Woo MS. Clinical findings and lung pathology in children with cystic fibrosis. Am J Respir Crit Care Med 2002;165:1172-1175.
-
(2002)
Am J Respir Crit Care Med
, vol.165
, pp. 1172-1175
-
-
Hamutcu, R.1
Rowland, J.M.2
Horn, M.V.3
Kaminsky, C.4
MacLaughlin, E.F.5
Starnes, V.A.6
Woo, M.S.7
-
16
-
-
0000963297
-
The pathology of cystic fibrosis
-
Hodson ME, Geddes DM, editors. London: Chapman and Hall
-
Sheppard MN. The pathology of cystic fibrosis. In: Hodson ME, Geddes DM, editors. Cystic fibrosis. London: Chapman and Hall; 1995. pp. 131-149.
-
(1995)
Cystic Fibrosis
, pp. 131-149
-
-
Sheppard, M.N.1
-
17
-
-
0028914085
-
Early pulmonary inflammation in infants with cystic fibrosis
-
Khan TZ, Wagener JS, Bost T, Martinez J, Accurso FJ, Riches DW. Early pulmonary inflammation in infants with cystic fibrosis. Am J Respir Crit Care Med 1995;151:1075-1082.
-
(1995)
Am J Respir Crit Care Med
, vol.151
, pp. 1075-1082
-
-
Khan, T.Z.1
Wagener, J.S.2
Bost, T.3
Martinez, J.4
Accurso, F.J.5
Riches, D.W.6
-
18
-
-
0141506124
-
Bronchoalveolar lavage fluid surfactant protein-A and surfactant protein-D are inversely related to inflammation in early cystic fibrosis
-
Noah TL, Murphy PC, Alink JJ, Leigh MW, Hull WM, Stahlman MT, Whitsett JA. Bronchoalveolar lavage fluid surfactant protein-A and surfactant protein-D are inversely related to inflammation in early cystic fibrosis. Am J Respir Crit Care Med 2003;168:685-691.
-
(2003)
Am J Respir Crit Care Med
, vol.168
, pp. 685-691
-
-
Noah, T.L.1
Murphy, P.C.2
Alink, J.J.3
Leigh, M.W.4
Hull, W.M.5
Stahlman, M.T.6
Whitsett, J.A.7
-
19
-
-
0014576029
-
The site of airway obstruction in cystic fibrosis
-
Mellins R. The site of airway obstruction in cystic fibrosis. Pediatrics 1969;44:315-318.
-
(1969)
Pediatrics
, vol.44
, pp. 315-318
-
-
Mellins, R.1
-
20
-
-
11144355490
-
The evolution of airway function in early childhood following clinical diagnosis of cystic fibrosis
-
Ranganathan SC, Stocks J, Dezateux C, Bush A, Wade A, Carr S, Castle R, Dinwiddie R, Hoo AF, Lum S, et al. The evolution of airway function in early childhood following clinical diagnosis of cystic fibrosis. Am J Respir Crit Care Med 2004;169:928-933.
-
(2004)
Am J Respir Crit Care Med
, vol.169
, pp. 928-933
-
-
Ranganathan, S.C.1
Stocks, J.2
Dezateux, C.3
Bush, A.4
Wade, A.5
Carr, S.6
Castle, R.7
Dinwiddie, R.8
Hoo, A.F.9
Lum, S.10
-
21
-
-
0036788775
-
Characterization of ion and fluid transport in human bronchioles
-
Blouquit S, Morel H, Hinnrasky J, Puchelle E, Chinet TC. Characterization of ion and fluid transport in human bronchioles. Am J Respir Cell Mol Biol 2002;27:503-510.
-
(2002)
Am J Respir Cell Mol Biol
, vol.27
, pp. 503-510
-
-
Blouquit, S.1
Morel, H.2
Hinnrasky, J.3
Puchelle, E.4
Chinet, T.C.5
-
22
-
-
33746657743
-
Regulation of airway surface liquid volume by human non-CF and CF distal airway epithelia
-
Blouquit S, Boucher RC. Regulation of airway surface liquid volume by human non-CF and CF distal airway epithelia [abstract]. Pediatr Pulmonol 2004(Suppl 28);217.
-
(2004)
Pediatr Pulmonol
, Issue.28 SUPPL.
, pp. 217
-
-
Blouquit, S.1
Boucher, R.C.2
-
23
-
-
33746607792
-
Ion transport in human non-CF and CF distal airway epithelium
-
Blouquit S, Naline E, Chinet TC. Ion transport in human non-CF and CF distal airway epithelium [abstract]. J Cyst Fibros 2002;S50-S51.
-
(2002)
J Cyst Fibros
-
-
Blouquit, S.1
Naline, E.2
Chinet, T.C.3
-
24
-
-
0022357460
-
A serum-free method for culturing normal human bronchial epithelial cells at clonal density
-
Lechner JF, LaVeck MA. A serum-free method for culturing normal human bronchial epithelial cells at clonal density. J Tiss Cult Methods 1985;9:43-48.
-
(1985)
J Tiss Cult Methods
, vol.9
, pp. 43-48
-
-
Lechner, J.F.1
LaVeck, M.A.2
-
25
-
-
0034885663
-
The CF salt controversy: In vivo observations and therapeutic approaches
-
Tarran R, Grubb BR, Parsons D, Picher M, Hirsh AJ, Davis CW, Boucher RC. The CF salt controversy: in vivo observations and therapeutic approaches. Mol Cell 2001;8:149-158.
-
(2001)
Mol Cell
, vol.8
, pp. 149-158
-
-
Tarran, R.1
Grubb, B.R.2
Parsons, D.3
Picher, M.4
Hirsh, A.J.5
Davis, C.W.6
Boucher, R.C.7
-
26
-
-
0022396481
-
Culture of human nasal epithelial cells on collagen matrix supports: A comparison of bioelectric properties of normal and cystic fibrosis epithelia
-
Yankaskas JR, Cotton CU, Knowles MR, Gatzy JT, Boucher RC. Culture of human nasal epithelial cells on collagen matrix supports: a comparison of bioelectric properties of normal and cystic fibrosis epithelia. Am Rev Respir Dis 1985;132:1281-1287.
-
(1985)
Am Rev Respir Dis
, vol.132
, pp. 1281-1287
-
-
Yankaskas, J.R.1
Cotton, C.U.2
Knowles, M.R.3
Gatzy, J.T.4
Boucher, R.C.5
-
27
-
-
0022588248
-
Abnormal respiratory epithelial ion transport in cystic fibrosis
-
Knowles MR, Stutts MJ, Yankaskas JR, Gatzy JT, Boucher RC. Abnormal respiratory epithelial ion transport in cystic fibrosis. Clin Chest Med 1986;7:285-297.
-
(1986)
Clin Chest Med
, vol.7
, pp. 285-297
-
-
Knowles, M.R.1
Stutts, M.J.2
Yankaskas, J.R.3
Gatzy, J.T.4
Boucher, R.C.5
-
28
-
-
0034762763
-
Isolation and culture of airway epithelial cells from chronically infected human lungs
-
Randell SH, Walstad L, Schwab UE, Grubb BR, Yankaskas JR. Isolation and culture of airway epithelial cells from chronically infected human lungs. In Vitro Cell Dev Biol Anim 2001;37:480-489.
-
(2001)
In Vitro Cell Dev Biol Anim
, vol.37
, pp. 480-489
-
-
Randell, S.H.1
Walstad, L.2
Schwab, U.E.3
Grubb, B.R.4
Yankaskas, J.R.5
-
29
-
-
0025990465
-
Radon dosimetry based on the depth distribution of nuclei in human and rat lungs
-
Mercer RR, Russel ML, Crapo JD. Radon dosimetry based on the depth distribution of nuclei in human and rat lungs. Health Phys 1991;61:117-130.
-
(1991)
Health Phys
, vol.61
, pp. 117-130
-
-
Mercer, R.R.1
Russel, M.L.2
Crapo, J.D.3
-
30
-
-
0024547744
-
Shunt resistance and ion permeabilities in normal and cystic fibrosis airway epithelia
-
Willumsen NJ, Boucher RC. Shunt resistance and ion permeabilities in normal and cystic fibrosis airway epithelia. Am J Physiol 1989;256:C1054-C1063.
-
(1989)
Am J Physiol
, vol.256
-
-
Willumsen, N.J.1
Boucher, R.C.2
-
31
-
-
0027379564
-
Sodium-permeable channels in the apical membrane of human nasal epithelial cells
-
Chinet TC, Fullton JM, Yankaskas JR, Boucher RC, Stutts MJ. Sodium-permeable channels in the apical membrane of human nasal epithelial cells. Am J Physiol 1993;265:C1050-C1060.
-
(1993)
Am J Physiol
, vol.265
-
-
Chinet, T.C.1
Fullton, J.M.2
Yankaskas, J.R.3
Boucher, R.C.4
Stutts, M.J.5
-
32
-
-
0026662657
-
Intracellular pH and its relationship to regulation of ion transport in normal and cystic fibrosis human nasal epithelia
-
Willumsen NJ, Boucher RC. Intracellular pH and its relationship to regulation of ion transport in normal and cystic fibrosis human nasal epithelia. J Physiol 1992;455:247-269.
-
(1992)
J Physiol
, vol.455
, pp. 247-269
-
-
Willumsen, N.J.1
Boucher, R.C.2
-
33
-
-
0032127980
-
The amiloride-inhibitable Na+ conductance is reduced by the cystic fibrosis transmembrane conductance regulator in normal but not in cystic fibrosis airways
-
Mall M, Bleich M, Greger R, Schreiber R, Kunzelmann K. The amiloride-inhibitable Na+ conductance is reduced by the cystic fibrosis transmembrane conductance regulator in normal but not in cystic fibrosis airways. J Clin Invest 1998;102:12-21.
-
(1998)
J Clin Invest
, vol.102
, pp. 12-21
-
-
Mall, M.1
Bleich, M.2
Greger, R.3
Schreiber, R.4
Kunzelmann, K.5
-
34
-
-
0021352368
-
Bioelectric properties and ion flow across excised human bronchi
-
Knowles M, Murray G, Shallal J, Askin F, Ranga V, Gatzy J, Boucher R. Bioelectric properties and ion flow across excised human bronchi. J Appl Physiol 1984;56:868-877.
-
(1984)
J Appl Physiol
, vol.56
, pp. 868-877
-
-
Knowles, M.1
Murray, G.2
Shallal, J.3
Askin, F.4
Ranga, V.5
Gatzy, J.6
Boucher, R.7
-
35
-
-
0033864526
-
Pharmacological modulation of ion transport across wild-type and δF508 CFTR-expressing human bronchial epithelia
-
Devor DC, Bridges RJ, Pilewski JM. Pharmacological modulation of ion transport across wild-type and δF508 CFTR-expressing human bronchial epithelia. Am J Physiol 2000;279:C461-C479.
-
(2000)
Am J Physiol
, vol.279
-
-
Devor, D.C.1
Bridges, R.J.2
Pilewski, J.M.3
-
36
-
-
0028218315
-
Characterization and comparison of ion transport across sheep and human airway epithelium
-
Steel DM, Graham A, Geddes DM, Alton EWFW. Characterization and comparison of ion transport across sheep and human airway epithelium. Epithelial Cell Biol 1994;3:24-31.
-
(1994)
Epithelial Cell Biol
, vol.3
, pp. 24-31
-
-
Steel, D.M.1
Graham, A.2
Geddes, D.M.3
Alton, E.W.F.W.4
-
37
-
-
0034796615
-
Ion transport by sheep small airways in a miniature chamber
-
Al-Bazzaz FJ, Gailey C. Ion transport by sheep small airways in a miniature chamber. Am J Physiol 2001;281:L1028-L1034.
-
(2001)
Am J Physiol
, vol.281
-
-
Al-Bazzaz, F.J.1
Gailey, C.2
-
38
-
-
0035157650
-
Expression of α-, β-, and γ-hENaC mRNA in the human nasal, bronchial, and distal lung epithelium
-
Pitkanen OM, Smith D, O'Brodovich H, Otulakowski G. Expression of α-, β-, and γ-hENaC mRNA in the human nasal, bronchial, and distal lung epithelium. Am J Respir Crit Care Med 2001;163:273-276.
-
(2001)
Am J Respir Crit Care Med
, vol.163
, pp. 273-276
-
-
Pitkanen, O.M.1
Smith, D.2
O'Brodovich, H.3
Otulakowski, G.4
-
39
-
-
0033951227
-
Early expression of β- and γ-subunits of epithelial sodium channel during human airway development
-
Gaillard D, Hinnrasky J, Coscoy S, Hofmann P, Matthay MA, Puchelle E, Barbry P. Early expression of β- and γ-subunits of epithelial sodium channel during human airway development. Am J Physiol 2000;278:L177-L184.
-
(2000)
Am J Physiol
, vol.278
-
-
Gaillard, D.1
Hinnrasky, J.2
Coscoy, S.3
Hofmann, P.4
Matthay, M.A.5
Puchelle, E.6
Barbry, P.7
-
41
-
-
0037277853
-
Functional interaction of CFTR and ENaC in sweat glands
-
Reddy M, Quinton PM. Functional interaction of CFTR and ENaC in sweat glands. Eur J Physiol 2003;445:499-503.
-
(2003)
Eur J Physiol
, vol.445
, pp. 499-503
-
-
Reddy, M.1
Quinton, P.M.2
-
42
-
-
27444444705
-
Normal and cystic fibrosis airway surface liquid homeostasis: The effects of phasic shear stress and viral infections
-
Tarran R, Button B, Picher M, Paradiso AM, Ribeiro CM, Lazarowski ER, Zhang L, Collins PL, Pickels RJ, Fredberg JJ, et al. Normal and cystic fibrosis airway surface liquid homeostasis: the effects of phasic shear stress and viral infections. J Biol Chem 2005;280:35751-35759.
-
(2005)
J Biol Chem
, vol.280
, pp. 35751-35759
-
-
Tarran, R.1
Button, B.2
Picher, M.3
Paradiso, A.M.4
Ribeiro, C.M.5
Lazarowski, E.R.6
Zhang, L.7
Collins, P.L.8
Pickels, R.J.9
Fredberg, J.J.10
-
43
-
-
0024465128
-
Chloride secretory response of cystic fibrosis human airway epithelia: Preservation of calcium but not protein kinase C- and A-dependent mechanisms
-
Boucher RC, Cheng EH, Paradiso AM, Stutts MJ, Knowles MR, Earp HS. Chloride secretory response of cystic fibrosis human airway epithelia: preservation of calcium but not protein kinase C- and A-dependent mechanisms. J Clin Invest 1989;84:1424-1431.
-
(1989)
J Clin Invest
, vol.84
, pp. 1424-1431
-
-
Boucher, R.C.1
Cheng, E.H.2
Paradiso, A.M.3
Stutts, M.J.4
Knowles, M.R.5
Earp, H.S.6
-
44
-
-
0026670029
-
Chloride secretory response to extracellular ATP in human normal and CF nasal epithelia
-
Clarke LL, Boucher RC. Chloride secretory response to extracellular ATP in human normal and CF nasal epithelia. Am J Physiol 1992;263:348-356.
-
(1992)
Am J Physiol
, vol.263
, pp. 348-356
-
-
Clarke, L.L.1
Boucher, R.C.2
-
45
-
-
0025874599
-
Activation by extracellular nucleotides of chloride secretion in the airway epithelia of patients with cystic fibrosis
-
Knowles MR, Clarke LL, Boucher RC. Activation by extracellular nucleotides of chloride secretion in the airway epithelia of patients with cystic fibrosis. N Engl J Med 1991;325:533-538.
-
(1991)
N Engl J Med
, vol.325
, pp. 533-538
-
-
Knowles, M.R.1
Clarke, L.L.2
Boucher, R.C.3
-
46
-
-
0037383908
-
+ channels in human normal and cystic fibrosis airway epithelia
-
+ channels in human normal and cystic fibrosis airway epithelia. Pediatr Res 2003;53:608-618.
-
(2003)
Pediatr Res
, vol.53
, pp. 608-618
-
-
Mall, M.1
Gonska, T.2
Thomas, J.3
Schreiber, R.4
Seydewitz, H.H.5
Kuehr, J.6
Brandis, M.7
Kunzelmann, K.8
-
48
-
-
1942421832
-
Liquid secretion properties of airway submucosal glands
-
Ballard ST, Inglis SK. Liquid secretion properties of airway submucosal glands. J Physiol 2004;556:1-10.
-
(2004)
J Physiol
, vol.556
, pp. 1-10
-
-
Ballard, S.T.1
Inglis, S.K.2
|