Monolysocardiolipins accumulate in Barth syndrome but do not lead to enhanced apoptosis

Journal of Lipid Research

Volumn 46, Issue 6, 2005, Pages 1182-1195

  Valianpour, Fredoen ^a   Mitsakos, Voula ^b   Schlemmer, Dimitri ^c   Towbin, Jeffrey A ^d   Taylor, Juliet M ^b   Ekert, Paul G ^e   Thorburn, David R ^b   Munnich, Arnold ^c   Wanders, Ronald J A ^a   Barth, Peter G ^a   Vaz, Frédéric M ^a  

^a UNIVERSITY OF AMSTERDAM   (Netherlands)

^b UNIVERSITY OF MELBOURNE   (Australia)

^c HÔPITAL NECKER ENFANTS MALADES   (France)

^d TEXAS CHILDREN S HOSPITAL   (United States)

^e ROYAL CHILDREN'S HOSPITAL   (Australia)

Author keywords

Cardiolipin; Lymphoblasts; Tafazzin

Indexed keywords

CARDIOLIPIN; LYSOPHOSPHOLIPID; BID PROTEIN, HUMAN; CARRIER PROTEIN; CYTOCHROME C; FAS ANTIGEN; MONOLYSOCARDIOLIPIN; NICOTINAMIDE ADENINE DINUCLEOTIDE ADENOSINE DIPHOSPHATE RIBOSYLTRANSFERASE; PHOSPHOLIPID; PROTEIN BID;

APOPTOSIS; ARTICLE; BARTH SYNDROME; CELL DEATH; CONTROLLED STUDY; FIBROBLAST; HEART; HUMAN; HUMAN CELL; LIPID ANALYSIS; LIPID COMPOSITION; LYMPHOBLAST; LYMPHOCYTE; MUSCLE; PRIORITY JOURNAL; THROMBOCYTE; ACYLATION; CARDIOMYOPATHY; CELL FRACTIONATION; CHEMISTRY; GENETIC LINKAGE; GROWTH DISORDER; HEART MUSCLE; HIGH PERFORMANCE LIQUID CHROMATOGRAPHY; IMMUNOBLOTTING; LEUKEMIA CELL LINE; LIPID METABOLISM; MASS SPECTROMETRY; METABOLISM; MITOCHONDRION; MUSCLE DISEASE; PROTEIN TERTIARY STRUCTURE; RECESSIVE GENE; SYNDROME; X CHROMOSOME;

ACYLATION; ANTIGENS, CD95; APOPTOSIS; BH3 INTERACTING DOMAIN DEATH AGONIST PROTEIN; CARDIOLIPINS; CARDIOMYOPATHIES; CARRIER PROTEINS; CELL DEATH; CHROMATOGRAPHY, HIGH PRESSURE LIQUID; CHROMOSOMES, HUMAN, X; CYTOCHROMES C; GENES, RECESSIVE; GROWTH DISORDERS; HUMANS; IMMUNOBLOTTING; JURKAT CELLS; LINKAGE (GENETICS); LIPID METABOLISM; LYMPHOCYTES; LYSOPHOSPHOLIPIDS; MASS SPECTROMETRY; MITOCHONDRIA; MUSCLES; MUSCULAR DISEASES; MYOCARDIUM; PHOSPHOLIPIDS; POLY(ADP-RIBOSE) POLYMERASES; PROTEIN STRUCTURE, TERTIARY; SUBCELLULAR FRACTIONS; SYNDROME;

EID: 24944563130     PISSN: 00222275     EISSN: 15397262     Source Type: Journal    
DOI: 10.1194/jlr.M500056-JLR200     Document Type: Article

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