In Vivo Regulation of Oxidative Phosphorylation in Cells Harboring a Stop-codon Mutation in Mitochondrial DNA-encoded Cytochrome c Oxidase Subunit I

Journal of Biological Chemistry

Volumn 276, Issue 50, 2001, Pages 46925-46932

  D'Aurelio, Marilena ^a   Pallotti, Francesco ^b   Barrientos, Antoni ^b   Gajewski, Carl D ^a   Kwong, Jennifer Q ^a   Bruno, Claudio ^c   Beal, M Flint ^a   Manfredi, Giovanni ^a  

^a WEILL CORNELL MEDICAL COLLEGE   (United States)

^b Och Spine at New York Presbyterian Hospitals   (United States)

^c UNIVERSITY OF GENOA   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

BIOSYNTHESIS; CELLS; DNA; POLYPEPTIDES; RNA;

PHOSPHORYLATION;

ADENOSINETRIPHOSPHATE;

ADENOSINE TRIPHOSPHATE; CYTOCHROME C OXIDASE; CYTOCHROME C OXIDASE 1; CYTOCHROME C OXIDASE 2; DNA; MESSENGER RNA; MITOCHONDRIAL DNA; POLYPEPTIDE; UNCLASSIFIED DRUG; GALACTOSE; OXYGEN; RNA;

ARTICLE; BIOCHEMISTRY; COMPLEX FORMATION; CONTROLLED STUDY; CORRELATION ANALYSIS; ENZYME REGULATION; ENZYME SUBUNIT; GENE MUTATION; HUMAN; HUMAN CELL; IN VIVO STUDY; MITOCHONDRIAL RESPIRATION; MOLECULAR DYNAMICS; OXIDATIVE PHOSPHORYLATION; PEPTIDE SYNTHESIS; PRIORITY JOURNAL; PROTEIN ASSEMBLY; PROTEIN PHOSPHORYLATION; PROTEIN PROCESSING; REGULATORY MECHANISM; STEADY STATE; STOP CODON; THROMBOCYTE; TRANSCRIPTION REGULATION; TRANSLATION REGULATION; BIOSYNTHESIS; CELL CULTURE; CELL LINE; CHEMISTRY; ELECTRON TRANSPORT; GENETIC TRANSCRIPTION; GENETICS; HYBRID CELL; IMMUNOBLOTTING; METABOLISM; MITOCHONDRION; MUTATION; NORTHERN BLOTTING; NUCLEOTIDE SEQUENCE; OXYGEN CONSUMPTION; PHOSPHORYLATION; RESTRICTION FRAGMENT LENGTH POLYMORPHISM; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; RNA TRANSLATION; TIME;

MAMMALIA;

ADENOSINE TRIPHOSPHATE; BLOOD PLATELETS; BLOTTING, NORTHERN; CELL LINE; CODON, TERMINATOR; CYTOCHROME-C OXIDASE; DNA MUTATIONAL ANALYSIS; DNA, MITOCHONDRIAL; ELECTRON TRANSPORT; GALACTOSE; HUMAN; HYBRID CELLS; IMMUNOBLOTTING; MITOCHONDRIA; MUTATION; OXYGEN; OXYGEN CONSUMPTION; PHOSPHORYLATION; POLYMORPHISM, RESTRICTION FRAGMENT LENGTH; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; RNA; RNA, MESSENGER; SUPPORT, NON-U.S. GOV'T; SUPPORT, U.S. GOV'T, P.H.S.; TIME FACTORS; TRANSCRIPTION, GENETIC; TRANSLATION, GENETIC; TUMOR CELLS, CULTURED;

EID: 0035861593     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M106429200     Document Type: Article

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