Canavan disease and the role of N-acetylaspartate in myelin synthesis

Molecular and Cellular Endocrinology

Volumn 252, Issue 1-2, 2006, Pages 216-223

  Namboodiri, Aryan M A ^a   Peethambaran, Arun ^a   Mathew, Raji ^a   Sambhu, Prasanth A ^a   Hershfield, Jeremy ^a   Moffett, John R ^a   Madhavarao, Chikkathur N ^a  

^a UNIFORMED SERVICES UNIVERSITY OF THE HEALTH SCIENCES   (United States)

Author keywords

Acetate hypothesis; Aspartoacylase; NAA; Oligodendrocytes; Spongiform degeneration

Indexed keywords

ACETIC ACID; ACETYL COENZYME A; AMINO ACID DERIVATIVE; ASPARTOACYLASE; CALCIUM ACETATE; MYELIN; N ACETYLASPARTIC ACID;

ARTICLE; AUTOSOMAL RECESSIVE DISORDER; BRAIN DEGENERATION; CANAVAN DISEASE; CELLULAR DISTRIBUTION; CENTRAL NERVOUS SYSTEM; DEACETYLATION; DEGENERATIVE DISEASE; ENZYME DEGRADATION; ENZYME INACTIVATION; ENZYME LOCALIZATION; ENZYME SYNTHESIS; GENE MUTATION; HUMAN; HYPOTHESIS; LIPOGENESIS; MYELINATION; NERVOUS SYSTEM DEVELOPMENT; NONHUMAN; OLIGODENDROGLIA; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN SYNTHESIS; PSYCHOMOTOR RETARDATION;

AGING; ANIMALS; ASPARTIC ACID; CANAVAN DISEASE; CENTRAL NERVOUS SYSTEM; HUMANS; MICE; MICE, KNOCKOUT; MYELIN BASIC PROTEINS;

EID: 33745194382     PISSN: 03037207     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.mce.2006.03.016     Document Type: Article

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