Inhibition of the electron transport chain and creatine kinase activity by ethylmalonic acid in human skeletal muscle

Metabolic Brain Disease

Volumn 21, Issue 1, 2006, Pages 11-19

  Barschak, Alethea G ^a   Ferreira, Gustavo Da C ^a   André, Karina R ^a   Schuck, Patrícia F ^a   Viegas, Carolina M ^a   Tonin, Anelise ^a   Filho, Carlos S Dutra ^a   Wyse, Angela T S ^a   Wannmacher, Clóvis M D ^a   Vargas, Carmen R ^a,b   Wajner, Moacir ^a,b,c  

^a FEDERAL UNIVERSITY OF RIO GRANDE DO SUL   (Brazil)

^b HOSPITAL DE CLÍNICAS DE PORTO ALEGRE   (Brazil)

^c UNIVERSIDADE LUTERANA DO BRASIL   (Brazil)

Author keywords

Energy metabolism; Ethylmalonic acid; Ethylmalonic aciduria; Skeletal muscle

Indexed keywords

ADENOSINE TRIPHOSPHATE; CREATINE KINASE; ETHYLMALONIC ACID; MALONIC ACID DERIVATIVE; UNCLASSIFIED DRUG;

ACIDURIA; ARTICLE; BRAIN DISEASE; CONTROLLED STUDY; DRUG EFFECT; ENERGY METABOLISM; ENZYME ACTIVITY; HUMAN; HUMAN CELL; HUMAN TISSUE; IN VITRO STUDY; MUSCLE HYPOTONIA; MYOPATHY; RESPIRATORY CHAIN; SKELETAL MUSCLE;

ACIDOSIS, LACTIC; ADENOSINE TRIPHOSPHATE; ADOLESCENT; ADULT; CREATINE KINASE; ELECTRON TRANSPORT CHAIN COMPLEX PROTEINS; ELECTRON TRANSPORT COMPLEX I; ELECTRON TRANSPORT COMPLEX II; ELECTRON TRANSPORT COMPLEX III; ELECTRON TRANSPORT COMPLEX IV; ENERGY METABOLISM; ENZYME ACTIVATION; HUMANS; MALONATES; MUSCLE, SKELETAL;

EID: 33745101968     PISSN: 08857490     EISSN: None     Source Type: Journal    
DOI: 10.1007/s11011-006-9000-y     Document Type: Article

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