Expanding view of phenotype and oxidative stress in Friedreich's ataxia patients with and without idebenone

Schweizer Archiv fur Neurologie und Psychiatrie

Volumn 157, Issue 4, 2006, Pages 169-176

  Arnold, P ^a   Boulat, O ^a   Maire, R ^a   Kuntzer, Thierry ^a  

^a LAUSANNE UNIVERSITY HOSPITAL   (Switzerland)

Author keywords

Cardiomyopathy; Clinical signs; Friedreich's ataxia; Hearing loss; ICARS; Idebenone; Malondialdehyde; Oxidative stress

Indexed keywords

IDEBENONE; MALONALDEHYDE; SUPEROXIDE;

ADOLESCENT; ADULT; ARTICLE; CARDIOMYOPATHY; CLINICAL ARTICLE; CLINICAL STUDY; CONTROLLED STUDY; DIABETES MELLITUS; DISEASE COURSE; DISEASE DURATION; DISEASE SEVERITY; DOSE RESPONSE; DRUG EFFECT; DRUG USE; DYSARTHRIA; ELECTROPHYSIOLOGY; FATIGUE; FEMALE; FOLLOW UP; FRIEDREICH ATAXIA; GENETIC ANALYSIS; GENOTYPE PHENOTYPE CORRELATION; HEARING LOSS; HUMAN; MALE; MULTIPLE LINEAR REGRESSION ANALYSIS; NUCLEOTIDE REPEAT; OXIDATIVE STRESS; PHENOTYPE; PTOSIS; SCORING SYSTEM; SKELETON MALFORMATION; VISUAL IMPAIRMENT;

EID: 33744980943     PISSN: 02587661     EISSN: None     Source Type: Journal    
DOI: 10.4414/sanp.2006.01730     Document Type: Article

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