-
1
-
-
0014139879
-
Brain metabolism during fasting
-
Owen O.E., Morgan A.P., Kemp H.G., Sullivan J.M., Herrera M.G., and Cahill Jr. G.F. Brain metabolism during fasting. J. Clin. Invest. 46 (1967) 1589-1595
-
(1967)
J. Clin. Invest.
, vol.46
, pp. 1589-1595
-
-
Owen, O.E.1
Morgan, A.P.2
Kemp, H.G.3
Sullivan, J.M.4
Herrera, M.G.5
Cahill Jr., G.F.6
-
3
-
-
0035203147
-
Fatty acid transport and mitochondrial oxidation disorders
-
Rinaldo P. Fatty acid transport and mitochondrial oxidation disorders. Semin. Liver Dis. 21 (2001) 489-500
-
(2001)
Semin. Liver Dis.
, vol.21
, pp. 489-500
-
-
Rinaldo, P.1
-
4
-
-
33745007865
-
-
C.R. Roe, J. Ding, Mitochondrial fatty acid oxidation, in: C.R. Scriver, A.L. Beaudet, W.S. Sly, D.Valle, (eds.), The Metabolic and Molecular Basis of Inherited Disease, 2001, pp. 2308-2311.
-
-
-
-
5
-
-
21144438020
-
Long-chain fatty acid oxidation during early human development
-
Oey N.A., den Boer M.E., Wijburg F.A., Vekemans M., Auge J., Steiner C., Wanders R.J., Wiaterham H.R., Ruiter J.P., and Attie-Bitach T. Long-chain fatty acid oxidation during early human development. Pediatr. Res. 57 (2005) 755-759
-
(2005)
Pediatr. Res.
, vol.57
, pp. 755-759
-
-
Oey, N.A.1
den Boer, M.E.2
Wijburg, F.A.3
Vekemans, M.4
Auge, J.5
Steiner, C.6
Wanders, R.J.7
Wiaterham, H.R.8
Ruiter, J.P.9
Attie-Bitach, T.10
-
6
-
-
33645654310
-
Fatty acid oxidation in the human fetus: implications for fetal and adult disease
-
Oey N.A., Ruiter J.P., Attie-Bitach T., IJlst L., Wanders R.J., and Wijburg F.A. Fatty acid oxidation in the human fetus: implications for fetal and adult disease. J. Inherit. Metab. Dis. 29 (2006) 71-75
-
(2006)
J. Inherit. Metab. Dis.
, vol.29
, pp. 71-75
-
-
Oey, N.A.1
Ruiter, J.P.2
Attie-Bitach, T.3
IJlst, L.4
Wanders, R.J.5
Wijburg, F.A.6
-
7
-
-
0036033276
-
Cloning and functional characterization of ACAD-9, a novel member of human acyl-CoA dehydrogenase family
-
Zhang J., Zhang W., Zou D., Chen G., Wan T., Zhang M., and Cao X. Cloning and functional characterization of ACAD-9, a novel member of human acyl-CoA dehydrogenase family. Biochem. Biophys. Res. Commun. 297 (2002) 1033-1042
-
(2002)
Biochem. Biophys. Res. Commun.
, vol.297
, pp. 1033-1042
-
-
Zhang, J.1
Zhang, W.2
Zou, D.3
Chen, G.4
Wan, T.5
Zhang, M.6
Cao, X.7
-
8
-
-
25444531436
-
HumaN acyl-CoA dehydrogenase-9 plays a novel role in the mitochondrial {beta}-oxidation of unsaturated fatty acids
-
Ensenauer R., He M., Willard J.M., Goetzman E.S., Corydon T.J., Vandahl B.B., Mohsen A.W., Isaya G., and Vockley J. HumaN acyl-CoA dehydrogenase-9 plays a novel role in the mitochondrial {beta}-oxidation of unsaturated fatty acids. J. Biol. Chem. 280 (2005) 32309-32316
-
(2005)
J. Biol. Chem.
, vol.280
, pp. 32309-32316
-
-
Ensenauer, R.1
He, M.2
Willard, J.M.3
Goetzman, E.S.4
Corydon, T.J.5
Vandahl, B.B.6
Mohsen, A.W.7
Isaya, G.8
Vockley, J.9
-
9
-
-
0344678385
-
Expression of the sonic hedgehog (SHH) gene during early human development and phenotypic expression of new mutations causing holoprosencephaly
-
Odent S., Atti-Bitach T., Blayau M., Mathieu M., Aug J., Delezo d.A., Gall J.Y., Le Marec B., Munnich A., David V., and Vekemans M. Expression of the sonic hedgehog (SHH) gene during early human development and phenotypic expression of new mutations causing holoprosencephaly. Hum. Mol. Genet. 8 (1999) 1683-1689
-
(1999)
Hum. Mol. Genet.
, vol.8
, pp. 1683-1689
-
-
Odent, S.1
Atti-Bitach, T.2
Blayau, M.3
Mathieu, M.4
Aug, J.5
Delezo, d.A.6
Gall, J.Y.7
Le Marec, B.8
Munnich, A.9
David, V.10
Vekemans, M.11
-
10
-
-
33745010156
-
-
D.G. Wilkinson, In situ hybridization: a pratical approach IRL press, Oxford, 1992.
-
-
-
-
11
-
-
0026458561
-
Human trifunctional protein deficiency: a new disorder of mitochondrial fatty acid beta-oxidation
-
Wanders R.J., IJlst L., Poggi F., Bonnefont J.P., Munnich A., Brivet M., Rabier D., and Saudubray J.M. Human trifunctional protein deficiency: a new disorder of mitochondrial fatty acid beta-oxidation. Biochem. Biophys. Res. Commun. 188 (1992) 1139-1145
-
(1992)
Biochem. Biophys. Res. Commun.
, vol.188
, pp. 1139-1145
-
-
Wanders, R.J.1
IJlst, L.2
Poggi, F.3
Bonnefont, J.P.4
Munnich, A.5
Brivet, M.6
Rabier, D.7
Saudubray, J.M.8
-
12
-
-
0032969056
-
Disorders of mitochondrial fatty acyl-CoA beta-oxidation
-
Wanders R.J., Vreken P., den Boer M.E., Wijburg F.A., van Gennip A.H., and IJlst L. Disorders of mitochondrial fatty acyl-CoA beta-oxidation. J. Inherit. Metab. Dis. 22 (1999) 442-487
-
(1999)
J. Inherit. Metab. Dis.
, vol.22
, pp. 442-487
-
-
Wanders, R.J.1
Vreken, P.2
den Boer, M.E.3
Wijburg, F.A.4
van Gennip, A.H.5
IJlst, L.6
-
13
-
-
6344235193
-
Mitochondrial fatty acid beta-oxidation in the human eye and brain: implications for the retinopathy of long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency
-
Tyni T., Paetau A., Strauss A.W., Middleton B., and Kivela T. Mitochondrial fatty acid beta-oxidation in the human eye and brain: implications for the retinopathy of long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency. Pediatr. Res. 56 (2004) 744-750
-
(2004)
Pediatr. Res.
, vol.56
, pp. 744-750
-
-
Tyni, T.1
Paetau, A.2
Strauss, A.W.3
Middleton, B.4
Kivela, T.5
-
14
-
-
0028982779
-
Mitochondrial beta-oxidation of 2-methyl fatty acids in rat liver
-
Mao L.F., Chu C., Luo M.J., Simon A., Abbas A.S., and Schulz H. Mitochondrial beta-oxidation of 2-methyl fatty acids in rat liver. Arch. Biochem. Biophys. 321 (1995) 221-228
-
(1995)
Arch. Biochem. Biophys.
, vol.321
, pp. 221-228
-
-
Mao, L.F.1
Chu, C.2
Luo, M.J.3
Simon, A.4
Abbas, A.S.5
Schulz, H.6
-
15
-
-
0032584506
-
2,6-Dimethylheptanoyl-CoA is a specific substrate for long-chain acyl-CoA dehydrogenase (LCAD): evidence for a major role of LCAD in branched-chain fatty acid oxidation
-
Wanders R.J., Denis S., Ruiter J.P., IJlst L., and Dacremont G. 2,6-Dimethylheptanoyl-CoA is a specific substrate for long-chain acyl-CoA dehydrogenase (LCAD): evidence for a major role of LCAD in branched-chain fatty acid oxidation. Biochim. Biophys. Acta 1393 (1998) 35-40
-
(1998)
Biochim. Biophys. Acta
, vol.1393
, pp. 35-40
-
-
Wanders, R.J.1
Denis, S.2
Ruiter, J.P.3
IJlst, L.4
Dacremont, G.5
-
16
-
-
0034738012
-
Long-chain acyl-CoA dehydrogenase is a key enzyme in the mitochondrial beta-oxidation of unsaturated fatty acids
-
Lea W., Abbas A.S., Sprecher H., Vockley J., and Schulz H. Long-chain acyl-CoA dehydrogenase is a key enzyme in the mitochondrial beta-oxidation of unsaturated fatty acids. Biochim. Biophys. Acta 1485 (2000) 121-128
-
(2000)
Biochim. Biophys. Acta
, vol.1485
, pp. 121-128
-
-
Lea, W.1
Abbas, A.S.2
Sprecher, H.3
Vockley, J.4
Schulz, H.5
-
17
-
-
0027771771
-
Tissue specific and developmental expression of rat long-and medium-chain acyl-CoA dehydrogenases
-
Hainline B.E., Kahlenbeck D.J., Grant J., and Strauss A.W. Tissue specific and developmental expression of rat long-and medium-chain acyl-CoA dehydrogenases. Biochim. Biophys. Acta 1216 (1993) 460-468
-
(1993)
Biochim. Biophys. Acta
, vol.1216
, pp. 460-468
-
-
Hainline, B.E.1
Kahlenbeck, D.J.2
Grant, J.3
Strauss, A.W.4
-
18
-
-
0029165220
-
RNA expression and chromosomal location of the mouse long-chain acyl-CoA dehydrogenase gene
-
Hinsdale M.E., Farmer S.C., Johnson K.R., Davisson M.T., Hamm D.A., Tolwani R.J., and Wood P.A. RNA expression and chromosomal location of the mouse long-chain acyl-CoA dehydrogenase gene. Genomics 28 (1995) 163-170
-
(1995)
Genomics
, vol.28
, pp. 163-170
-
-
Hinsdale, M.E.1
Farmer, S.C.2
Johnson, K.R.3
Davisson, M.T.4
Hamm, D.A.5
Tolwani, R.J.6
Wood, P.A.7
|