Long-chain fatty acid oxidation during early human development

Pediatric Research

Volumn 57, Issue 6, 2005, Pages 755-759

  Oey, Nadia A ^a   Den Boer, Margarethe E J ^a   Wijburg, Frits A ^a,c   Vekemans, Michel ^b   Augé, Joëlle ^b   Steiner, Céline ^b   Wanders, Ronald J A ^a   Waterham, Hans R ^a   Ruiter, Jos P N ^a   Attié Bitach, Tania ^b  

^a UNIVERSITY OF AMSTERDAM   (Netherlands)

^b HÔPITAL NECKER ENFANTS MALADES   (France)

^c EMMA CHILDREN S HOSPITAL   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

CARNITINE PALMITOYL COENZYME A TRANSFERASE 2; CARNITINE PALMITOYLTRANSFERASE; LONG CHAIN 3 HYDROXYACYL COENZYME A DEHYDROGENASE; LONG CHAIN FATTY ACID; MESSENGER RNA; MITOCHONDRIAL TRIFUNCTIONAL PROTEIN; OXIDOREDUCTASE; PROTEIN; UNCLASSIFIED DRUG; VERY LONG CHAIN ACYL COENZYME A DEHYDROGENASE;

ARTICLE; CARDIOMYOPATHY; CENTRAL NERVOUS SYSTEM; CLINICAL FEATURE; CONTROLLED STUDY; EMBRYO; EMBRYO DEVELOPMENT; ENZYME ACTIVITY; ENZYME DEFICIENCY; FATTY ACID OXIDATION; FETUS; FETUS DEVELOPMENT; GENE EXPRESSION; HEART; HELLP SYNDROME; HUMAN; HUMAN TISSUE; HYPOGLYCEMIA; HYPOKETOTIC HYPOGLYCEMIA; IN SITU HYBRIDIZATION; INTRAUTERINE GROWTH RETARDATION; LIVER; MITOCHONDRIAL RESPIRATION; PERIPHERAL NEUROPATHY; PREGNANCY COMPLICATION; PRIORITY JOURNAL; RETINA NEUROEPITHELIAL LAYER; RETINOPATHY; RHABDOMYOLYSIS;

3-HYDROXYACYL COA DEHYDROGENASES; ACYL-COA DEHYDROGENASE, LONG-CHAIN; BASE SEQUENCE; CARNITINE O-PALMITOYLTRANSFERASE; DNA; FATTY ACIDS; FEMALE; FETAL DEVELOPMENT; HUMANS; IN SITU HYBRIDIZATION; LIPID METABOLISM, INBORN ERRORS; MATERNAL-FETAL EXCHANGE; MULTIENZYME COMPLEXES; OXIDATION-REDUCTION; PLACENTA; PREGNANCY; RNA, MESSENGER; TISSUE DISTRIBUTION;

EID: 21144438020     PISSN: 00313998     EISSN: None     Source Type: Journal    
DOI: 10.1203/01.PDR.0000161413.42874.74     Document Type: Article

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