Living donor liver transplantation for noncirrhotic inheritable metabolic liver diseases: Impact of the use of heterozygous donors

Transplantation

Volumn 80, Issue 5, 2005, Pages 623-628

  Morioka, Daisuke ^a   Takada, Yasutsugu ^a   Kasahara, Mureo ^a   Ito, Takashi ^a   Uryuhara, Kenji ^a   Ogawa, Kohei ^a   Egawa, Hiroto ^a   Tanaka, Koichi ^a  

^a KYOTO UNIVERSITY HOSPITAL   (Japan)

Author keywords

Donor selection; Inherited diseases; Liver transplantation; Noncirrhotic metabolic liver disease; Organ donation

Indexed keywords

METHYLMALONIC ACID; ORNITHINE CARBAMOYLTRANSFERASE; PROPIONIC ACID;

ADOLESCENT; ADULT; ARTICLE; CITRULLINEMIA; CLINICAL ARTICLE; CRIGLER NAJJAR SYNDROME; DISORDERS OF AMINO ACID AND PROTEIN METABOLISM; EVALUATION; FAMILIAL AMYLOID POLYNEUROPATHY; FEMALE; GROWTH RETARDATION; HETEROZYGOSITY; HETEROZYGOTE; HUMAN; INFANT; LIVER DISEASE; LIVER TRANSPLANTATION; LIVING DONOR; MALE; METABOLIC DISORDER; METHYLMALONIC ACIDEMIA; MORBIDITY; MORTALITY; NEUROLOGIC DISEASE; PREOPERATIVE CARE; PRIORITY JOURNAL; PROPIONIC ACIDEMIA; TREATMENT OUTCOME;

ACIDOSIS; ADOLESCENT; ADULT; AMYLOID NEUROPATHIES, FAMILIAL; CHILD; CHILD, PRESCHOOL; CITRULLINEMIA; CRIGLER-NAJJAR SYNDROME; FEMALE; HETEROZYGOTE; HUMANS; INFANT; LIVER DISEASES; LIVER TRANSPLANTATION; LIVING DONORS; MALE; METABOLISM, INBORN ERRORS; MIDDLE AGED; ORNITHINE CARBAMOYLTRANSFERASE DEFICIENCY DISEASE; SURVIVAL RATE; TREATMENT OUTCOME;

EID: 25444503514     PISSN: 00411337     EISSN: None     Source Type: Journal    
DOI: 10.1097/01.tp.0000167995.46778.72     Document Type: Article

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