Measurement of ATP production in mitochondrial disorders

Journal of Inherited Metabolic Disease

Volumn 29, Issue 1, 2006, Pages 86-91

  Shepherd, R K ^a   Checcarelli, N ^b   Naini, A ^b   De Vivo, D C ^b   DiMauro, S ^b   Sue, C M ^a  

^a UNIVERSITY OF SYDNEY   (Australia)

^b Och Spine at New York Presbyterian Hospitals   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ADENOSINE TRIPHOSPHATE; CELL NUCLEUS DNA; MITOCHONDRIAL DNA; MUTANT PROTEIN;

ADOLESCENT; ADULT; AGED; ARTICLE; CELL LINE; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; CORRELATION ANALYSIS; DISORDERS OF MITOCHONDRIAL FUNCTIONS; DNA DETERMINATION; FEMALE; FIBROBLAST; GENE MUTATION; GENETIC LOAD; HUMAN; HUMAN CELL; HUMAN TISSUE; MALE; MELAS SYNDROME; PHENOTYPE; PROTEIN SYNTHESIS;

ADENOSINE TRIPHOSPHATE; ADOLESCENT; ADULT; AGED; CHILD; CHILD, PRESCHOOL; FEMALE; FIBROBLASTS; HUMANS; INFANT; MALE; MELAS SYNDROME; MIDDLE AGED; MITOCHONDRIAL DISEASES; MUTATION;

EID: 33645689666     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-006-0148-8     Document Type: Article

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