Anesthetic management of patients with ornithine transcarbamylase deficiency

Paediatric Anaesthesia

Volumn 16, Issue 3, 2006, Pages 333-337

  Schmidt, Joachim ^a   Kroeber, Stefanie ^a   Irouschek, Andrea ^a   Birkholz, Torsten ^a   Schroth, Michael ^a   Albrecht, Sven ^a  

^a UNIVERSITY OF ERLANGEN NUREMBERG   (Germany)

Author keywords

Alternative pathway therapy; General anesthesia; Hyperammonemia; Ornithine transcarbamylase deficiency; Perioperative management

Indexed keywords

ARGININE; ARYLBUTYRIC ACID DERIVATIVE; BENZOIC ACID; CITRULLINE; FENTANYL; GLYCOPYRRONIUM BROMIDE; ISOFLURANE; KETAMINE; MIDAZOLAM; ORNITHINE CARBAMOYLTRANSFERASE; ROPIVACAINE; VECURONIUM;

AMMONIA BLOOD LEVEL; ARTICLE; ARTIFICIAL VENTILATION; CALORIC DENSITY; CASE REPORT; CHROMOSOME ANALYSIS; CLINICAL FEATURE; DISEASE SEVERITY; DISORDERS OF AMINO ACID AND PROTEIN METABOLISM; EXTUBATION; FEMALE; GENERAL ANESTHESIA; HUMAN; LABORATORY TEST; METABOLIC DISORDER; MONOZYGOTIC TWINS; NEUROLOGIC EXAMINATION; PRIORITY JOURNAL;

ANESTHESIA, GENERAL; ANESTHETICS, COMBINED; CATHETERIZATION, CENTRAL VENOUS; CATHETERS, INDWELLING; CHILD, PRESCHOOL; DISEASES IN TWINS; FEMALE; FENTANYL; HUMANS; INTRAOPERATIVE CARE; ISOFLURANE; KETAMINE; MIDAZOLAM; ORNITHINE CARBAMOYLTRANSFERASE DEFICIENCY DISEASE; PARENTERAL NUTRITION; PREANESTHETIC MEDICATION;

EID: 33645307680     PISSN: 11555645     EISSN: 14609592     Source Type: Journal    
DOI: 10.1111/j.1460-9592.2005.01695.x     Document Type: Article

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