Living related liver transplantation for patients with ornithine transcarbarnylase deficiency

Japanese Journal of Anesthesiology

Volumn 46, Issue 6, 1997, Pages 783-787

  Tazuke, Misako ^a   Murakawa, Masahiro ^a   Nakao, Shin Ichi ^a   Mukaida, Kumiko ^a   Toda, Hiroshi ^a   Mori, Kenjiro ^a  

^a KYOTO UNIVERSITY HOSPITAL   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

BENZOIC ACID; FENTANYL; MIDAZOLAM; ORNITHINE CARBAMOYLTRANSFERASE;

ANESTHESIOLOGICAL TECHNIQUES; ARTICLE; CLINICAL ARTICLE; ENZYME DEFICIENCY; FEMALE; HUMAN; HYPERAMMONEMIA; LIVER TRANSPLANTATION; PRESCHOOL CHILD; PROTEIN RESTRICTION; TREATMENT OUTCOME; TREATMENT PLANNING; X CHROMOSOME LINKAGE;

AMINO ACID METABOLISM, INBORN ERRORS; AMMONIA; ANESTHESIA, INTRAVENOUS; ANESTHETICS, COMBINED; ANESTHETICS, INTRAVENOUS; CHILD, PRESCHOOL; FEMALE; FENTANYL; HUMANS; LIVER TRANSPLANTATION; MIDAZOLAM; MONITORING, INTRAOPERATIVE; ORNITHINE CARBAMOYLTRANSFERASE;

EID: 0030872630     PISSN: 00214892     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

References (11)

1. Largilliere C, Houssin D, Gottrand F, et al: Liver transplantation for ornithine transcarbamylase deficiency in a girl. J Pediatr 115: 415, 1989
2. Broelsch CE, Emond JC, Whitington PF, et al: Application of reduced-size liver transplants as split grafts, auxiliary orthotopic grafts, and living related segmentai transplants. Ann Surg 212: 368, 1990
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4. Hasegawa T, Tzakis AG, Todo S, et al: Orthotopic liver transplantation for ornithine transcarbamylase deficiency with hyperammonemic encephalopathy. J Pediatr Surg 30: 863, 1995
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