Treatment of ornithine transcarbamylase deficiency in girls by auxiliary liver transplantation: Conceptual changes in a living-donor program

Journal of Pediatric Surgery

Volumn 33, Issue 12, 1998, Pages 1753-1756

  Kasahara, Mureo ^a   Kiuchi, Tetsuya ^a   Uryuhara, Kenji ^a   Ogura, Yasuhiro ^a   Takakura, Koji ^a   Egawa, Hiroto ^a   Asonuma, Katsuhiro ^a   Uemoto, Shinji ^a   Inomata, Yukihiro ^a   Tanaka, Koichi ^a  

^a KYOTO UNIVERSITY HOSPITAL   (Japan)

Author keywords

Auxiliary transplantation; Hyperammonemia; Liver failure; Living related liver transplantation; Ornithine transcarbamylase deficiency

Indexed keywords

ORNITHINE CARBAMOYLTRANSFERASE; STEROID; TACROLIMUS;

ARTICLE; CASE REPORT; CHILD; COMA; ENZYME DEFICIENCY; FEMALE; HETEROZYGOSITY; HUMAN; HYPERAMMONEMIA; IMMUNOSUPPRESSIVE TREATMENT; LIVER DYSFUNCTION; LIVER TRANSPLANTATION; LIVING DONOR; PRIORITY JOURNAL; SURGICAL TECHNIQUE; X CHROMOSOME LINKED DISORDER;

EID: 13144279265     PISSN: 00223468     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0022-3468(98)90278-0     Document Type: Article

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