-
1
-
-
0001752544
-
Cystic fibrosis
-
Scriver CR, Beaudet AL, Sly WS, Valle D, eds. New York: McGraw-Hill
-
Welsh M, Ramsey B, Accurso F, Cutting G. Cystic fibrosis. In: Scriver CR, Beaudet AL, Sly WS, Valle D, eds. The Metabolic and Molecular Basis of Inherited Disease, 8th ed. New York: McGraw-Hill; 2001:5121-588.
-
(2001)
The Metabolic and Molecular Basis of Inherited Disease, 8th Ed.
, pp. 5121-5588
-
-
Welsh, M.1
Ramsey, B.2
Accurso, F.3
Cutting, G.4
-
2
-
-
0037460729
-
Cystic fibrosis
-
Ratjen F, Doring G. Cystic fibrosis. Lancet 2003;361:681-689.
-
(2003)
Lancet
, vol.361
, pp. 681-689
-
-
Ratjen, F.1
Doring, G.2
-
3
-
-
0024424270
-
Identification of the cystic fibrosis gene: Cloning and characterization of complementary DNA
-
Riodan JR, Rommens JM, Kerem B. Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA. Science 1989;245:1066-1073.
-
(1989)
Science
, vol.245
, pp. 1066-1073
-
-
Riodan, J.R.1
Rommens, J.M.2
Kerem, B.3
-
4
-
-
0025760318
-
Genomic DNA sequence of the cystic fibrosis transmembrane conductance regulator
-
Zielinski J, Rozmahel R, Bozon D. Genomic DNA sequence of the cystic fibrosis transmembrane conductance regulator. Genomics 1991;10:241-248.
-
(1991)
Genomics
, vol.10
, pp. 241-248
-
-
Zielinski, J.1
Rozmahel, R.2
Bozon, D.3
-
5
-
-
0003452177
-
-
The Cystic Fibrosis Genetic Analysis Consortium. Cystic Fibrosis Mutation Data Base, www.genet.sickkids.on.ca/cftr/ Accessed November 26, 2002.
-
Cystic Fibrosis Mutation Data Base
-
-
-
6
-
-
1342333784
-
Diagnosis of CF despite normal or borderline sweat chloride
-
Leigh MW. Diagnosis of CF despite normal or borderline sweat chloride. Paediatr. Respir. Rev. 2004;5:357-359.
-
(2004)
Paediatr. Respir. Rev.
, vol.5
, pp. 357-359
-
-
Leigh, M.W.1
-
7
-
-
0038663174
-
Effect of genotype on phenotype and mortality in cystic fibrosis: A retrospective cohort study
-
McKone EF, Emerson SS, Edwards KL, Aitken ML. Effect of genotype on phenotype and mortality in cystic fibrosis: a retrospective cohort study. Lancet 2003;361:1671-1676.
-
(2003)
Lancet
, vol.361
, pp. 1671-1676
-
-
McKone, E.F.1
Emerson, S.S.2
Edwards, K.L.3
Aitken, M.L.4
-
9
-
-
0036529082
-
Endotoxin activity and inflammatory markers in the airways of young patients with cystic fibrosis
-
Muhlebach MS, Noah TL. Endotoxin activity and inflammatory markers in the airways of young patients with cystic fibrosis. Am. J. Respir. Care Med. 2002;165:911-915.
-
(2002)
Am. J. Respir. Care Med.
, vol.165
, pp. 911-915
-
-
Muhlebach, M.S.1
Noah, T.L.2
-
11
-
-
0029686250
-
Cytokine soup: Making sense of inflammation in cystic fibrosis
-
Richman-Eisenstadt J. Cytokine soup: making sense of inflammation in cystic fibrosis. Pediatr. Pulmonol. 1996;21:3-5.
-
(1996)
Pediatr. Pulmonol.
, vol.21
, pp. 3-5
-
-
Richman-Eisenstadt, J.1
-
12
-
-
21444461227
-
Cytokine levels in sputum of cystic fibrosis patients before and after antibiotic therapy
-
Colombo C, Constantini D, Rocchi A, Cariani L, Tirelli S, Calori G, Copreni E, and Conese M. Cytokine levels in sputum of cystic fibrosis patients before and after antibiotic therapy. Pediatr. Pulmonol. 2005;40:15-21.
-
(2005)
Pediatr. Pulmonol.
, vol.40
, pp. 15-21
-
-
Colombo, C.1
Constantini, D.2
Rocchi, A.3
Cariani, L.4
Tirelli, S.5
Calori, G.6
Copreni, E.7
Conese, M.8
-
13
-
-
23644460295
-
The role of airway epithelium and blood neutrophils in the inflammatory response in cystic fibrosis
-
Epub ahead of print
-
Terheggen-Lagro SW, Rijkers GT, Van Der Ent CK. The role of airway epithelium and blood neutrophils in the inflammatory response in cystic fibrosis. J Cystic Fibrosis 2005;17 [Epub ahead of print].
-
(2005)
J. Cystic Fibrosis
, vol.17
-
-
Terheggen-Lagro, S.W.1
Rijkers, G.T.2
Van Der Ent, C.K.3
-
14
-
-
0036743565
-
Cell and cytokine profile in nasal secretions in cystic fibrosis
-
Bergoin C, Gosset P, Lamblin C, Bolard F, Turck D, Tonnel AB, Wallaert B. Cell and cytokine profile in nasal secretions in cystic fibrosis. J. Cystic. Fibrosis 2002;1:110-115.
-
(2002)
J. Cystic. Fibrosis
, vol.1
, pp. 110-115
-
-
Bergoin, C.1
Gosset, P.2
Lamblin, C.3
Bolard, F.4
Turck, D.5
Tonnel, A.B.6
Wallaert, B.7
-
15
-
-
18944368921
-
Differential cytokine profile in children with cystic fibrosis
-
Brazova J, Sediva A, Pospisilova D, Vavrova V, Pohunek P, Macek M, Bartunkova J, Lauschmann H. Differential cytokine profile in children with cystic fibrosis. Clin. Immunol. 2005;115:210-215.
-
(2005)
Clin. Immunol.
, vol.115
, pp. 210-215
-
-
Brazova, J.1
Sediva, A.2
Pospisilova, D.3
Vavrova, V.4
Pohunek, P.5
Macek, M.6
Bartunkova, J.7
Lauschmann, H.8
-
16
-
-
13644274627
-
Cytokines and inflammatory mediators in cystic fibrosis
-
Courtney JM, Ennis M, Elborn JS. Cytokines and inflammatory mediators in cystic fibrosis. J. Cystic Fibrosis 2004;3:223-231.
-
(2004)
J. Cystic Fibrosis
, vol.3
, pp. 223-231
-
-
Courtney, J.M.1
Ennis, M.2
Elborn, J.S.3
-
17
-
-
0030615201
-
Nuclear factor κB-a pivotal transcription factor in chronic inflammatory diseases
-
Barnes TL, Konstan MW. Nuclear factor κB-a pivotal transcription factor in chronic inflammatory diseases. N. Engl. J Med. 1997;336:1066-1071.
-
(1997)
N. Engl. J Med.
, vol.336
, pp. 1066-1071
-
-
Barnes, T.L.1
Konstan, M.W.2
-
18
-
-
14944344881
-
NF-kappaB activation and sustained 1L-8 gene expression in primary cultures of cystic fibrosis airway epithelial cells stimulated with Pseudomonas aeruginosa
-
Joseph T, Look D, Ferkol T. NF-kappaB activation and sustained 1L-8 gene expression in primary cultures of cystic fibrosis airway epithelial cells stimulated with Pseudomonas aeruginosa. Am. J. Physiol. Lung Cell. Mol. Physiol. 2005;288:L471-479.
-
(2005)
Am. J. Physiol. Lung Cell. Mol. Physiol.
, vol.288
-
-
Joseph, T.1
Look, D.2
Ferkol, T.3
-
19
-
-
0030816336
-
Neutrophil receptors for interleulin-8 and related CXC chemokines
-
Murphy PM. Neutrophil receptors for interleulin-8 and related CXC chemokines. Semin. Hematol. 1997;34:311-318.
-
(1997)
Semin. Hematol.
, vol.34
, pp. 311-318
-
-
Murphy, P.M.1
-
20
-
-
0024317984
-
Production of interleukin-8 by human dermal fibroblasts and keratinocytes in response to interleukin-1 or tumor necrosis factor
-
Larsen CG, Anderson AO, Oppenheim JJ, Matsushima K. Production of interleukin-8 by human dermal fibroblasts and keratinocytes in response to interleukin-1 or tumor necrosis factor. Immunology 1989;68:31-36.
-
(1989)
Immunology
, vol.68
, pp. 31-36
-
-
Larsen, C.G.1
Anderson, A.O.2
Oppenheim, J.J.3
Matsushima, K.4
-
21
-
-
0036936445
-
Relationships among specific viral pathogens, virus-induced interleukin-8, and respiratory symptoms in infancy
-
Gern JE, Martin MS, Anclam KA. Relationships among specific viral pathogens, virus-induced interleukin-8, and respiratory symptoms in infancy. Pediatr. Allergy Immunol. 2002;13:386-393.
-
(2002)
Pediatr. Allergy Immunol.
, vol.13
, pp. 386-393
-
-
Gern, J.E.1
Martin, M.S.2
Anclam, K.A.3
-
22
-
-
0842307140
-
Immunomodulating effect of antimicrobial agents on cytokine production by human polymorphonuclear neutrophils
-
Reato G, Cuffini AM, Tullio V. Immunomodulating effect of antimicrobial agents on cytokine production by human polymorphonuclear neutrophils. Int. J. Antimicrob. Agents 2004;23:150-154.
-
(2004)
Int. J. Antimicrob. Agents
, vol.23
, pp. 150-154
-
-
Reato, G.1
Cuffini, A.M.2
Tullio, V.3
-
23
-
-
0343134087
-
Effects of interferons alpha and gamma on cytokine production and phenotypic pattern of human bronchial epithelial cells
-
Striz I, Mio T, Adachi Y, Carnevali S, Romberger DJ, Rennard SI. Effects of interferons alpha and gamma on cytokine production and phenotypic pattern of human bronchial epithelial cells. Int. J. Immunopharmacol. 2000;22:573-585.
-
(2000)
Int. J. Immunopharmacol.
, vol.22
, pp. 573-585
-
-
Striz, I.1
Mio, T.2
Adachi, Y.3
Carnevali, S.4
Romberger, D.J.5
Rennard, S.I.6
-
25
-
-
0031911965
-
The concept of type 1 and type 2 helper T cells and their cytokines in humans
-
Del Prete G. The concept of type 1 and type 2 helper T cells and their cytokines in humans. Int. Rev. Immunol. 1998;16:427-455.
-
(1998)
Int. Rev. Immunol.
, vol.16
, pp. 427-455
-
-
Del Prete, G.1
-
27
-
-
0028172198
-
Effect of TGF-beta on interferon-gamma-induced HLA-DR expression in human retinal pigment epithelial cells
-
Gabrielian K, Osusky R, Sippy BD, Ryan SJ, Hinton DR. Effect of TGF-beta on interferon-gamma-induced HLA-DR expression in human retinal pigment epithelial cells. Invest. Ophthalmol. Vis. Sci. 1994;35:4253-4259.
-
(1994)
Invest. Ophthalmol. Vis. Sci.
, vol.35
, pp. 4253-4259
-
-
Gabrielian, K.1
Osusky, R.2
Sippy, B.D.3
Ryan, S.J.4
Hinton, D.R.5
-
28
-
-
0026033453
-
Regulation of MHC class II antigen expression opposing effects of tumor necrosis factor-α on IFN-γ-induced HLA-DR and Ia expression depends on the maturation and differentiation stage of the cell
-
Watanabe Y, Jacob CO. Regulation of MHC class II antigen expression opposing effects of tumor necrosis factor-α on IFN-γ-induced HLA-DR and Ia expression depends on the maturation and differentiation stage of the cell. J. Immunol. 1991;146:899-905.
-
(1991)
J. Immunol.
, vol.146
, pp. 899-905
-
-
Watanabe, Y.1
Jacob, C.O.2
-
29
-
-
4244174334
-
Expression of apoptotic and inflammatory markers in the human conjunctival epithelium
-
Baudouin C, De Saint Jean M, Brignole F. Expression of apoptotic and inflammatory markers in the human conjunctival epithelium (ARVO Abstract). Invest. Ophthalmol Vis. Sci. 1998;39:551.
-
(1998)
Invest. Ophthalmol. Vis. Sci.
, vol.39
, pp. 551
-
-
Baudouin, C.1
De Saint Jean, M.2
Brignole, F.3
-
30
-
-
0035738646
-
Interleukin-8 concentrations in conjunctival epithelium brush cytology samples correlate with neutrophil, eosinophil infiltration, and corneal damage
-
Miyoshi T, Fukagawa K, Shimmura S. Interleukin-8 concentrations in conjunctival epithelium brush cytology samples correlate with neutrophil, eosinophil infiltration, and corneal damage. Cornea 2001;20:743-747.
-
(2001)
Cornea
, vol.20
, pp. 743-747
-
-
Miyoshi, T.1
Fukagawa, K.2
Shimmura, S.3
-
31
-
-
0032709209
-
Altered cytokine balance in the tear fluid and conjunctiva of patients with Sjögren's syndrome keratoconjunctivitis sicca
-
Pflufelder SC, Jones D, Ji Z. Altered cytokine balance in the tear fluid and conjunctiva of patients with Sjögren's syndrome keratoconjunctivitis sicca. Curr. Eye Res. 1999;19:201-211.
-
(1999)
Curr. Eye Res.
, vol.19
, pp. 201-211
-
-
Pflufelder, S.C.1
Jones, D.2
Ji, Z.3
-
32
-
-
0027379904
-
IL-8 gene expression in cultures of human corneal epithelial cells and keratocytes
-
Cubbit CL, Tang Q, Monteiro CA. IL-8 gene expression in cultures of human corneal epithelial cells and keratocytes. Invest. Ophthalmol. Vis. Sci. 1993;34:3199-3206.
-
(1993)
Invest. Ophthalmol. Vis. Sci.
, vol.34
, pp. 3199-3206
-
-
Cubbit, C.L.1
Tang, Q.2
Monteiro, C.A.3
-
33
-
-
0033953402
-
Tear levels of interferon-γ, interleukin (IL)-2, IL-4 and IL-5 in patients with vernal keratoconjunctivitis, atopic keratoconjunctivitis and allergic conjunctivitis
-
Uchio E, Ono SY, Ikezawa Z, Ohno S. Tear levels of interferon-γ, interleukin (IL)-2, IL-4 and IL-5 in patients with vernal keratoconjunctivitis, atopic keratoconjunctivitis and allergic conjunctivitis. Clin. Exp. Allergy 2000;30:103-109.
-
(2000)
Clin. Exp. Allergy
, vol.30
, pp. 103-109
-
-
Uchio, E.1
Ono, S.Y.2
Ikezawa, Z.3
Ohno, S.4
-
34
-
-
0032128069
-
Cytokine and lipid inflammatory mediator profile of human tears contact lens associated inflammatory diseases
-
Thakur A, Willcox MDP. Cytokine and lipid inflammatory mediator profile of human tears contact lens associated inflammatory diseases. Exp. Eye Res. 1998;67:9-19.
-
(1998)
Exp. Eye Res.
, vol.67
, pp. 9-19
-
-
Thakur, A.1
Willcox, M.D.P.2
-
35
-
-
0031913950
-
The proinflammatory cytokines and arachidonic acid metabolites in human overnight tears: Homeostatic mechanisms
-
Thakur A, Willcox MDP, Stapleton F. The proinflammatory cytokines and arachidonic acid metabolites in human overnight tears: homeostatic mechanisms. J. Clin. Immunol. 1998;18:61-70.
-
(1998)
J. Clin. Immunol.
, vol.18
, pp. 61-70
-
-
Thakur, A.1
Willcox, M.D.P.2
Stapleton, F.3
-
36
-
-
0042283246
-
Long-term study of 105 patients with cystic fibrosis. Studies made over a 5 to 14 year period
-
Schwachmann H, Kulczycki LL. Long-term study of 105 patients with cystic fibrosis. Studies made over a 5 to 14 year period. Am. J. Dis. Child. 1958;96:6-15.
-
(1958)
Am. J. Dis. Child.
, vol.96
, pp. 6-15
-
-
Schwachmann, H.1
Kulczycki, L.L.2
-
38
-
-
0025787337
-
Presence of NAP-1/IL-8 in synovial fluids indicates a possible pathogenic role in rheumatoid arthritis
-
Peichl P, Cheska M, Effenberger F. Presence of NAP-1/IL-8 in synovial fluids indicates a possible pathogenic role in rheumatoid arthritis. Scand. J. Immunol. 1991;34:333-339.
-
(1991)
Scand. J. Immunol.
, vol.34
, pp. 333-339
-
-
Peichl, P.1
Cheska, M.2
Effenberger, F.3
-
39
-
-
0033059090
-
Murine endotoxin-induced uveitis, but not immune complex-induced uveitis, is dependent on the IL-8 receptor homolog
-
Brito BE, O'Rourke LM, Pan Y. Murine endotoxin-induced uveitis, but not immune complex-induced uveitis, is dependent on the IL-8 receptor homolog. Curr. Eye Res. 1999;19:76-85.
-
(1999)
Curr. Eye Res.
, vol.19
, pp. 76-85
-
-
Brito, B.E.1
O'Rourke, L.M.2
Pan, Y.3
-
40
-
-
0032979083
-
Ocular signs and vitamin a status in patients with cystic fibrosis treated with daily vitamin a supplements
-
Ansari EA, Sahni K, Etherington CH. Ocular signs and vitamin A status in patients with cystic fibrosis treated with daily vitamin A supplements. Br. J. Ophthalmol. 1999;83:688-691.
-
(1999)
Br. J. Ophthalmol.
, vol.83
, pp. 688-691
-
-
Ansari, E.A.1
Sahni, K.2
Etherington, C.H.3
-
41
-
-
0034106759
-
Determination of T-cell subpopulations and intracellular cytokine production (interleukin-2, interleukin-4, and interferon-gamma) by cord blood T-lymphocytes of neonates from atopic and non-atopic parents
-
Hagendorens MM, Van Bever HP, Schuerwehg AJ. Determination of T-cell subpopulations and intracellular cytokine production (interleukin-2, interleukin-4, and interferon-gamma) by cord blood T-lymphocytes of neonates from atopic and non-atopic parents. Pediatr. Allergy Immunol. 2000;11:12-19.
-
(2000)
Pediatr. Allergy Immunol.
, vol.11
, pp. 12-19
-
-
Hagendorens, M.M.1
Van Bever, H.P.2
Schuerwehg, A.J.3
|