Ultrastructure of lamellar bodies in congenital surfactant deficiency

Ultrastructural Pathology

Volumn 29, Issue 6, 2005, Pages 503-509

  Edwards, V ^d   Cutz, E ^a   Viero, S ^d   Moore, A M ^a,b   Nogee, L ^c  

^a HOSPITAL FOR SICK CHILDREN   (Canada)

^b UNIVERSITY OF TORONTO   (Canada)

^c JOHNS HOPKINS HOSPITAL   (United States)

^d NONE

Author keywords

ABCA3 mutations; Alveolar type II cells; Respiratory failure in term neonates; SP B deficiency

Indexed keywords

LUNG SURFACTANT;

ARTICLE; CASE REPORT; CELL ULTRASTRUCTURE; CONGENITAL LUNG SURFACTANT DEFICIENCY; CYTOPLASM; DISEASE SEVERITY; FEMALE; GENE MUTATION; HUMAN; HUMAN CELL; HUMAN TISSUE; INFANT; LAMELLAR BODY; LIPID TRANSPORT; LUNG ALVEOLUS CELL TYPE 2; LUNG ALVEOLUS PROTEINOSIS; LUNG BIOPSY; LUNG DISEASE; MALE; MICROSCOPY; MUTATION; PRIORITY JOURNAL; RESPIRATORY FAILURE; STRUCTURE ANALYSIS; TRANSMISSION ELECTRON MICROSCOPY; ULTRASTRUCTURE;

ATP-BINDING CASSETTE TRANSPORTERS; FEMALE; HUMANS; INFANT, NEWBORN; LUNG DISEASES; MALE; MICROSCOPY, ELECTRON, TRANSMISSION; MUTATION; PULMONARY ALVEOLI; PULMONARY SURFACTANT-ASSOCIATED PROTEIN B; RESPIRATORY DISTRESS SYNDROME, NEWBORN;

EID: 28844503843     PISSN: 01913123     EISSN: 15210758     Source Type: Journal    
DOI: 10.1080/01913120500323480     Document Type: Article

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