Phenotypic variability in human prion diseases

Neuropathology and Applied Neurobiology

Volumn 31, Issue 6, 2005, Pages 565-579

  Ironside, James W ^a,b   Ritchie, D L ^a   Head, M W ^a  

^a UNIVERSITY OF EDINBURGH   (United Kingdom)

^b WESTERN GENERAL HOSPITAL   (United Kingdom)

Author keywords

Creutzfeldt Jakob disease; Neuropathology; Prion diseases; Prion protein; Variant Creutzfeldt Jakob disease; Western blot

Indexed keywords

ISOPROTEIN; PRION PROTEIN;

BOVINE SPONGIFORM ENCEPHALOPATHY; BRAIN REGION; CHEMICAL ANALYSIS; CLINICAL FEATURE; CODON; CREUTZFELDT JAKOB DISEASE; DISEASE CLASSIFICATION; FAMILIAL DISEASE; GENE INSERTION; GENETIC POLYMORPHISM; GENETIC RISK; GENOTYPE; HETEROZYGOSITY; HOMOZYGOSITY; HUMAN; MODEL; MOLECULAR BIOLOGY; NEUROPATHOLOGY; NEUROPROTECTION; NONHUMAN; PHENOTYPIC VARIATION; PRION DISEASE; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN FUNCTION; PROTEIN VARIANT; REVIEW; RISK FACTOR;

CREUTZFELDT-JAKOB SYNDROME; HUMANS; PHENOTYPE; PRIONS; VARIATION (GENETICS);

EID: 27944438917     PISSN: 03051846     EISSN: 13652990     Source Type: Journal    
DOI: 10.1111/j.1365-2990.2005.00697.x     Document Type: Review

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