Mass spectrometric analysis reveals changes in phospholipid, neutral sphingolipid and sulfatide molecular species in progressive epilepsy with mental retardation, EPMR, brain: A case study

Journal of Neurochemistry

Volumn 95, Issue 3, 2005, Pages 609-617

  Hermansson, Martin ^a   Käkelä, Reijo ^a,b   Berghäll, Maria ^a   Lehesjoki, Anna Elina ^c   Somerharju, Pentti ^a   Lahtinen, Ulla ^c  

^a UNIVERSITY OF HELSINKI   (Finland)

^b UNIVERSITY OF EASTERN FINLAND   (Finland)

^c UNIVERSITY OF HELSINKI   (Finland)

Author keywords

CLN8; Liquid chromatography mass spectrometry; Neuronal ceroid lipofuscinosis; Phospholipid; Progressive epilepsy with mental retardation; Sphingolipid

Indexed keywords

CERAMIDE; CHOLESTEROL; GALACTOSYLCERAMIDE; GLYCEROPHOSPHOLIPID; LACTOSYLCERAMIDE; LONG CHAIN FATTY ACID; PHOSPHATIDYLETHANOLAMINE; PHOSPHATIDYLSERINE; PHOSPHOLIPID; SPHINGOLIPID; SULFATIDE;

ADULT; ARTICLE; CASE REPORT; CONTROLLED STUDY; EPILEPSY; HUMAN; HUMAN TISSUE; LIPID COMPOSITION; LIPID PEROXIDATION; LIQUID CHROMATOGRAPHY; MALE; MASS SPECTROMETRY; MEMBRANE STABILIZATION; MENTAL DEFICIENCY; NEURONAL CEROID LIPOFUSCINOSIS; NEUROTRANSMISSION; PRIORITY JOURNAL; PROGRESSIVE EPILEPSY WITH MENTAL RETARDATION;

ADULT; AGED; ANTIGENS, CD; BRAIN; CHOLESTEROL; EPILEPSY; GALACTOSYLCERAMIDES; HUMANS; LACTOSYLCERAMIDES; MALE; MASS SPECTROMETRY; MEMBRANE PROTEINS; MENTAL RETARDATION; MIDDLE AGED; NEURONAL CEROID-LIPOFUSCINOSES; NEUTRAL GLYCOSPHINGOLIPIDS; PHOSPHATIDYLETHANOLAMINES; PHOSPHATIDYLSERINES; SPHINGOMYELINS; SULFOGLYCOSPHINGOLIPIDS;

EUKARYOTA;

EID: 27644473103     PISSN: 00223042     EISSN: None     Source Type: Journal    
DOI: 10.1111/j.1471-4159.2005.03376.x     Document Type: Article

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