Biochemical and pathological evaluation of long-lived mice with globoid cell leukodystrophy after bone marrow transplantation

Molecular Genetics and Metabolism

Volumn 86, Issue 1-2, 2005, Pages 150-159

  Luzi, Paola ^a   Rafi, Mohammad A ^a   Zaka, Mariam ^a   Han, Zhi Rao ^a   Curtis, Mark ^a   Vanier, Marie T ^b   Wenger, David A ^a  

^a THOMAS JEFFERSON UNIVERSITY   (United States)

^b CENTRE HOSPITALIER LYON SUD   (France)

Author keywords

Bone marrow transplantation; Galactocerebrosidase; Globoid cell leukodystrophy; Krabbe disease; Lysosomal storage disease; Myelin; Psychosine; Twitcher mouse

Indexed keywords

GALACTOSYLCERAMIDASE; MYELIN; PSYCHOSINE;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BONE MARROW TRANSPLANTATION; BRAIN; BRAIN REGION; CHEMICAL ANALYSIS; CONTROLLED STUDY; EDEMA; ENZYME ACTIVITY; FEMALE; GLOBOID CELL LEUKODYSTROPHY; LIFESPAN; LIVER; MALE; MOUSE; NERVE FIBER; NERVE FIBER MEMBRANE; NONHUMAN; NORMAL VALUE; PRIORITY JOURNAL; REMYELINIZATION; SCIATIC NERVE; STAINING; TRANSGENIC MOUSE;

ANIMALS; BONE MARROW TRANSPLANTATION; LEUKODYSTROPHY, GLOBOID CELL; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MICROSCOPY, ELECTRON;

ALLIUM CEPA; ANIMALIA; CANIS FAMILIARIS; MUS MUSCULUS;

EID: 26244456612     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2005.06.023     Document Type: Article

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