Periodontal status in two siblings with severe congenital neutropenia: Diagnosis and mutational analysis of the cases

Journal of Periodontology

Volumn 76, Issue 5, 2005, Pages 837-844

  Hakki, Sema S ^a   Aprikyan, Andrew A G ^b   Yildirim, Sibel ^a   Aydinbelge, Mustafa ^a   Gokalp, Alparslan ^a   Ucar, Canan ^a   Guran, Sefik ^c   Koseoglu, Vedat ^c   Ataoglu, Tamer ^a   Somerman, Martha J ^d  

^a SELCUK UNIVERSITY   (Turkey)

^b UNIVERSITY OF WASHINGTON SCHOOL OF MEDICINE   (United States)

^c GULHANE SCHOOL OF MEDICINE   (Turkey)

^d UNIVERSITY OF WASHINGTON   (United States)

Author keywords

Autosomal recessive syndrome; Congenital diagnosis; Delivery of dental care; Kostmann syndrome diagnosis; Neutropenia

Indexed keywords

AMIKACIN; ANTIBIOTIC AGENT; COTRIMOXAZOLE; MEROPENEM;

ANAMNESIS; ARTICLE; BACTERIAL INFECTION; BONE MARROW BIOPSY; CASE REPORT; CLINICAL EXAMINATION; CONSULTATION; CYTOGENETICS; DIAGNOSTIC VALUE; DISEASE SEVERITY; FEMALE; FOLLOW UP; GINGIVA BLEEDING; GINGIVITIS; HUMAN; HUMAN CELL; LEUKOCYTE COUNT; LYMPHADENITIS; MALE; MOUTH HYGIENE; MUTATIONAL ANALYSIS; NEUTROPENIA; PERIODONTITIS; PRESCHOOL CHILD; RECURRENT DISEASE; SIBLING; TOOTH EXTRACTION;

BACTERIAL INFECTIONS; CELL DIFFERENTIATION; CHILD; CHILD, PRESCHOOL; CONSANGUINITY; DENTAL CARIES; DENTITION, PRIMARY; FEMALE; HUMANS; LEUKOCYTE COUNT; MALE; NEUTROPENIA; NEUTROPHILS; PEDIGREE; PERIODONTAL DISEASES; RECURRENCE; SIBLINGS; TOOTH LOSS; TOOTH MOBILITY;

EID: 20744440502     PISSN: 00223492     EISSN: None     Source Type: Journal    
DOI: 10.1902/jop.2005.76.5.837     Document Type: Article

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