Cofactor treatment improves ATP synthetic capacity in patients with oxidative phosphorylation disorders

Molecular Genetics and Metabolism

Volumn 81, Issue 4, 2004, Pages 263-272

  Marriage, Barbara J ^a,b   Clandinin, M Thomas ^a   Macdonald, Ian M ^a   Glerum, D Moira ^a  

^a UNIVERSITY OF ALBERTA   (Canada)

^b ABBOTT LABORATORIES   (United States)

Author keywords

ATP; Coenzyme Q10; Mitochondrial disease; Oxidative phosphorylation

Indexed keywords

ADENOSINE TRIPHOSPHATE; ALPHA TOCOPHEROL; ANTIOXIDANT; ASCORBIC ACID; CARNITINE; MENADIONE; NICOTINIC ACID; PHYTOMENADIONE; RIBOFLAVIN; THIAMINE; UBIDECARENONE; VITAMIN K GROUP;

ADOLESCENT; ADULT; ARTICLE; CHILD; CLINICAL ARTICLE; CLINICAL FEATURE; CONTROLLED STUDY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; DRUG EFFECT; EVALUATION; FEMALE; HUMAN; LYMPHOCYTE; MALE; OXIDATIVE PHOSPHORYLATION; OXIDATIVE PHOSPHORYLATION DISORDER; PRIORITY JOURNAL; SIDE EFFECT; TREATMENT OUTCOME;

ADENOSINE TRIPHOSPHATE; ADOLESCENT; ADULT; ANTIOXIDANTS; CHILD; DOSE-RESPONSE RELATIONSHIP, DRUG; FEMALE; HUMANS; LYMPHOCYTES; MALE; MIDDLE AGED; MITOCHONDRIAL DISEASES; UBIQUINONE;

EID: 1842523325     PISSN: 10967192     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.ymgme.2003.12.008     Document Type: Article

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