Differential trafficking of the Niemann-Pick C1 and 2 proteins highlights distinct roles in late endocytic lipid trafficking

Acta Paediatrica, International Journal of Paediatrics, Supplement

Volumn 92, Issue 443, 2003, Pages 63-73

  Zhang, M ^a   Sun, M ^b   Dwyer, N K ^a   Comly, M E ^b   Patel, S C ^c   Sundaram, R ^c   Hanover, J A ^a   Blanchette Mackie, E J ^a  

^a NATIONAL INSTITUTE OF DIABETES AND DIGESTIVE AND KIDNEY DISEASES   (United States)

^b NATIONAL INSTITUTE OF NEUROLOGICAL DISORDERS AND STROKE   (United States)

^c VETERANS AFFAIRS MEDICAL CENTER   (United States)

Author keywords

Cholesterol trafficking; Glycolipid trafficking; Niemann Pick type C; NPC1 protein; NPC2 protein

Indexed keywords

CHIMERIC PROTEIN; CHOLESTEROL; GANGLIOSIDE GM2; GLYCOLIPID; NIEMANN PICK C1 PROTEIN; NIEMANN PICK C2 PROTEIN; PROTEIN; PROTEIN DERIVATIVE; RED FLUORESCENT PROTEIN; UNCLASSIFIED DRUG;

ANIMAL CELL; BIOACCUMULATION; CELLULAR DISTRIBUTION; CHO CELL; CONFERENCE PAPER; CONTROLLED STUDY; FIBROBLAST CULTURE; HUMAN; HUMAN CELL; HUMAN CELL CULTURE; IMMUNOCYTOCHEMISTRY; LIPID ANALYSIS; LIPID DEGRADATION; LIPID METABOLISM; LYSOSOME; MOLECULAR DYNAMICS; NONHUMAN; PHENOTYPIC PLASTICITY; PHENOTYPIC VARIATION; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN LOCALIZATION;

EID: 1642496888     PISSN: 08035326     EISSN: None     Source Type: Journal    
DOI: 10.1111/j.1651-2227.2003.tb00224.x     Document Type: Conference Paper

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