Peroxisome proliferator activated receptor δ (PPARδ) agonist but not PPARα corrects carnitine palmitoyl transferase 2 deficiency in human muscle cells

Journal of Clinical Endocrinology and Metabolism

Volumn 90, Issue 3, 2005, Pages 1791-1797

  Djouadi, Fatima ^a   Aubey, Flore ^a   Schlemmer, Dimitri ^a   Bastin, Jean ^a  

^a HÔPITAL NECKER ENFANTS MALADES   (France)

Author keywords

[No Author keywords available]

Indexed keywords

BEZAFIBRATE; CARNITINE PALMITOYL TRANSFERASE 2; CARNITINE PALMITOYLTRANSFERASE; FATTY ACID; GW 0742; GW 7647; MESSENGER RNA; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR AGONIST; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR ALPHA; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR DELTA; UNCLASSIFIED DRUG; ACYLCARNITINE; ANTILIPEMIC AGENT; BUTYRIC ACID DERIVATIVE; CARBANILAMIDE DERIVATIVE; CARNITINE; DIAGNOSTIC AGENT; DRUG DERIVATIVE; GW 742; PALMITIC ACID; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR GAMMA; THIAZOLE DERIVATIVE; TRITIUM;

ARTICLE; CELL STIMULATION; CONTROLLED STUDY; DRUG TARGETING; ENZYME DEFICIENCY; FATTY ACID OXIDATION; GENE EXPRESSION; GENETIC TRANSCRIPTION; HUMAN; HUMAN CELL; HYPOTHESIS; MYOBLAST; PRIORITY JOURNAL; ADULT; CELL CULTURE; DOSE RESPONSE; DRUG EFFECT; DRUG POTENTIATION; ENZYME ACTIVATION; ENZYMOLOGY; GENETICS; METABOLISM; MUSCLE CELL; POINT MUTATION;

ADULT; ANTILIPEMIC AGENTS; BEZAFIBRATE; BUTYRIC ACIDS; CARNITINE; CARNITINE O-PALMITOYLTRANSFERASE; CELLS, CULTURED; DOSE-RESPONSE RELATIONSHIP, DRUG; ENZYME ACTIVATION; GENE EXPRESSION; HUMANS; MUSCLE FIBERS; PALMITIC ACID; PHENYLUREA COMPOUNDS; POINT MUTATION; PPAR GAMMA; THIAZOLES; TRITIUM;

EID: 15944376229     PISSN: 0021972X     EISSN: None     Source Type: Journal    
DOI: 10.1210/jc.2004-1936     Document Type: Article

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