Physiological and pathological aspects of GSH metabolism

Acta Paediatrica, International Journal of Paediatrics

Volumn 94, Issue 2, 2005, Pages 132-137

  Njålsson, Runa ^a   Norgren, Svante ^a  

^a KAROLINSKA UNIVERSITY HOSPITAL   (Sweden)

Author keywords

5 oxoprolinase; Glutathione; Glutathione synthetase deficiency; Haemolytic anaemia; Metabolic acidosis

Indexed keywords

2 OXO 4 THIAZOLIDINECARBOXYLIC ACID; 5 OXOPROLINASE; ACETYLCYSTEINE; ALPHA TOCOPHEROL; ASCORBIC ACID; BICARBONATE; CITRIC ACID; CREATINE; GAMMA GLUTAMYLCYSTEINE; GAMMA GLUTAMYLTRANSFERASE; GLUTAMATE CYSTEINE LIGASE; GLUTATHIONE; GLUTATHIONE SYNTHASE; PYROGLUTAMIC ACID; THIAZOLIDINE DERIVATIVE; TROMETAMOL;

ANTIOXIDANT ACTIVITY; ASTHMA; AUTOSOMAL RECESSIVE DISORDER; CARBOHYDRATE DIET; CATALYSIS; CENTRAL NERVOUS SYSTEM DISEASE; CHILDHOOD MORTALITY; CLINICAL FEATURE; CORRELATION ANALYSIS; DIAGNOSTIC TEST; DISEASE COURSE; ENZYME ACTIVITY; ENZYME DEFICIENCY; FIBROBLAST CULTURE; GENE MUTATION; GENOTYPE; GLUTATHIONE METABOLISM; HEMOLYTIC ANEMIA; HUMAN; INBORN ERROR OF METABOLISM; LUNG DYSPLASIA; METABOLIC ACIDOSIS; NECROTIZING ENTEROCOLITIS; NEUROTOXICITY; NONHUMAN; OXIDATIVE STRESS; PATENT DUCTUS ARTERIOSUS; PHENOTYPE; PRIORITY JOURNAL; RETROLENTAL FIBROPLASIA; REVIEW;

ACIDOSIS; ANEMIA, HEMOLYTIC; GLUTATHIONE; GLUTATHIONE SYNTHASE; HUMANS; INFANT, NEWBORN; INFANT, PREMATURE, DISEASES; METABOLISM, INBORN ERRORS; PYROGLUTAMATE HYDROLASE;

EID: 14844313300     PISSN: 08035253     EISSN: 16512227     Source Type: Journal    
DOI: 10.1080/08035250410025285     Document Type: Review

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