5-oxoprolinuria in patients with and without defects in the γ-glutamyl cycle

European Journal of Pediatrics

Volumn 158, Issue 3, 1999, Pages 221-225

  Mayatepek, E ^a  

^a UNIVERSITY HOSPITAL HEIDELBERG   (Germany)

Author keywords

Glutamyl cycle; 5 Oxoprolinuria; Glutathione metabolism

Indexed keywords

5 OXOPROLINASE; GLUTATHIONE; GLUTATHIONE SYNTHASE; METHYLMALONIC ACID; PROPIONIC ACID; PYROGLUTAMIC ACID;

5 OXOPROLINURIA; ACIDURIA; ARTICLE; CLINICAL ARTICLE; ENZYME DEFICIENCY; GLUTATHIONE METABOLISM; HOMOCYSTINURIA; HUMAN; INBORN ERROR OF METABOLISM; METHYLMALONIC ACIDEMIA; PREMATURITY; PRIORITY JOURNAL; PROPIONIC ACIDEMIA; STEVENS JOHNSON SYNDROME; UREA CYCLE; URINARY EXCRETION;

ADOLESCENT; ADULT; CHILD; CHILD, PRESCHOOL; GLUTATHIONE; GLUTATHIONE SYNTHASE; HUMANS; INFANT; METABOLISM, INBORN ERRORS; PYROGLUTAMATE HYDROLASE; PYRROLIDONECARBOXYLIC ACID;

EID: 0033003636     PISSN: 03406199     EISSN: None     Source Type: Journal    
DOI: 10.1007/s004310051054     Document Type: Article

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