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Volumn 217, Issue 1, 2004, Pages 83-88

Nerve conduction velocity measurements reveal the functional deficit in ceramide galactosyl transferase-deficient (cgt-/-) mice

Author keywords

Dysmyelinosis; Galactocerebroside and sulfatide (cgt ) deficient mouse model; Gene targeting; Myelin membrane lipid bilayer; Nerve conduction velocity

Indexed keywords

CERAMIDE GLUCOSYLTRANSFERASE;

EID: 0346849959     PISSN: 0022510X     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.jns.2003.09.004     Document Type: Article
Times cited : (8)

References (24)
  • 1
    • 0027440258 scopus 로고
    • Ceramide UDP galactosyltransferase from myelinating rat brain: Purification, cloning, and expression
    • Schulte S., Stoffel W. Ceramide UDP galactosyltransferase from myelinating rat brain: purification, cloning, and expression. Proc. Natl. Acad. Sci. U. S. A. 90:1993;10265-10269.
    • (1993) Proc. Natl. Acad. Sci. U. S. A. , vol.90 , pp. 10265-10269
    • Schulte, S.1    Stoffel, W.2
  • 2
    • 0031983184 scopus 로고    scopus 로고
    • Composition and biophysical properties of myelin lipid define the neurological defects in galactocerebroside-sulfatide-deficient mice
    • Bosio A., Binczek E., Haupt W.F., Stoffel W. Composition and biophysical properties of myelin lipid define the neurological defects in galactocerebroside-sulfatide-deficient mice. J. Neurochem. 70:1998;308-315.
    • (1998) J. Neurochem. , vol.70 , pp. 308-315
    • Bosio, A.1    Binczek, E.2    Haupt, W.F.3    Stoffel, W.4
  • 3
    • 0031983184 scopus 로고    scopus 로고
    • Biophysical properties of myelin lipid define the neurological defects in galactocerebroside and sulfatide-deficient mice
    • Bosio A., Binczek E., Haupt W.F., Stoffel W. Biophysical properties of myelin lipid define the neurological defects in galactocerebroside and sulfatide-deficient mice. J. Neurochem. 70:1998;308-315.
    • (1998) J. Neurochem. , vol.70 , pp. 308-315
    • Bosio, A.1    Binczek, E.2    Haupt, W.F.3    Stoffel, W.4
  • 4
    • 0009652097 scopus 로고
    • Versuche über die Fortpflanzungsgeschwindigkeit in den motorischen Nerven des Menschen
    • Helmholtz M., Baxt N. Versuche über die Fortpflanzungsgeschwindigkeit in den motorischen Nerven des Menschen. Kgl Preuss Ber Akad Wissensch Berlin. 1867;228-234.
    • (1867) Kgl Preuss Ber Akad Wissensch Berlin , pp. 228-234
    • Helmholtz, M.1    Baxt, N.2
  • 5
    • 78651012619 scopus 로고
    • The human electromyogram in response to nerve stimulation and the conduction velocity of motor axons
    • Hodes R., Larrabee M., German W. The human electromyogram in response to nerve stimulation and the conduction velocity of motor axons. Arch. Neurol. Psychiat. (Chic). 60:1948;340-365.
    • (1948) Arch. Neurol. Psychiat. (Chic) , vol.60 , pp. 340-365
    • Hodes, R.1    Larrabee, M.2    German, W.3
  • 6
    • 0029851157 scopus 로고    scopus 로고
    • Functional breakdown of the lipid bilayer of the myelin membrane in central and peripheral nervous system by disrupted galactocerebroside synthesis
    • Bosio A., Binczek E., Stoffel W. Functional breakdown of the lipid bilayer of the myelin membrane in central and peripheral nervous system by disrupted galactocerebroside synthesis. Proc. Natl. Acad. Sci.U. S. A. 93:1996;13280-13285.
    • (1996) Proc. Natl. Acad. Sci.U. S. A. , vol.93 , pp. 13280-13285
    • Bosio, A.1    Binczek, E.2    Stoffel, W.3
  • 7
    • 0021358883 scopus 로고
    • Formation of germ-line chimaeras from embryo-derived teratocarcinoma cell lines
    • Bradley A., Evans M., Kaufman M., Robertson E. Formation of germ-line chimaeras from embryo-derived teratocarcinoma cell lines. Nature. 309:1984;255-256.
    • (1984) Nature , vol.309 , pp. 255-256
    • Bradley, A.1    Evans, M.2    Kaufman, M.3    Robertson, E.4
  • 8
    • 0003799070 scopus 로고
    • B. Hogan, F. Costantini, & E. Lacy. New York: Cold Spring Harbor Laboratory
    • Hogan B., Costantini F., Lacy E. Manipulating the mouse embryo. 1986;Cold Spring Harbor Laboratory, New York.
    • (1986) Manipulating the Mouse Embryo
  • 9
    • 0034882140 scopus 로고    scopus 로고
    • Schwann cell myelination occurred without basal lamina formation in laminin (α2 chain mutant dy3K/dy3K) mice
    • Nagakawa M., Miyagoe-Suzuki Y., Ikezoe K., Miyata Y., Nonaka I., Harii S. Schwann cell myelination occurred without basal lamina formation in laminin (α2 chain mutant dy3K/dy3K) mice. Glia. 35:2001;101-110.
    • (2001) Glia , vol.35 , pp. 101-110
    • Nagakawa, M.1    Miyagoe-Suzuki, Y.2    Ikezoe, K.3    Miyata, Y.4    Nonaka, I.5    Harii, S.6
  • 11
    • 0034804805 scopus 로고    scopus 로고
    • Nerve conduction abnormalities in aging mice deficient for myelin-associated glycoprotein
    • Weiss M.D., Luciano C.A., Quarles R.H. Nerve conduction abnormalities in aging mice deficient for myelin-associated glycoprotein. Muscle Nerve. 24:2001;1380-1387.
    • (2001) Muscle Nerve , vol.24 , pp. 1380-1387
    • Weiss, M.D.1    Luciano, C.A.2    Quarles, R.H.3
  • 12
    • 0016691170 scopus 로고
    • Electrophysiological properties of spinal motoneurons of normal and dystrophic mice
    • Huizar P., Kuno M., Miyata Y. Electrophysiological properties of spinal motoneurons of normal and dystrophic mice. J. Physiol. 248:1975;231-246.
    • (1975) J. Physiol. , vol.248 , pp. 231-246
    • Huizar, P.1    Kuno, M.2    Miyata, Y.3
  • 13
    • 0030201110 scopus 로고    scopus 로고
    • Molecular cloning and characterization of the mouse CGT gene encoding UDP-galactose ceramide-galactosyltransferase (cerebroside synthetase)
    • Bosio A., Binczek E., Stoffel W. Molecular cloning and characterization of the mouse CGT gene encoding UDP-galactose ceramide-galactosyltransferase (cerebroside synthetase). Genomics. 35:1996;223-226.
    • (1996) Genomics , vol.35 , pp. 223-226
    • Bosio, A.1    Binczek, E.2    Stoffel, W.3
  • 14
    • 0033200305 scopus 로고    scopus 로고
    • Subtle roles of neural cell adhesion molecule and myelin-associated glycoprotein during Schwann cell spiraling in P0-deficient mice
    • Carenini S., Montag D., Schachner M., Martini R. Subtle roles of neural cell adhesion molecule and myelin-associated glycoprotein during Schwann cell spiraling in P0-deficient mice. Glia. 27:1999;203-212.
    • (1999) Glia , vol.27 , pp. 203-212
    • Carenini, S.1    Montag, D.2    Schachner, M.3    Martini, R.4
  • 15
    • 0019828169 scopus 로고
    • Shiverer: An autosomal recessive mutant mouse with myelin deficiency
    • Chernoff G. Shiverer: an autosomal recessive mutant mouse with myelin deficiency. J. Heredity. 72:1981;128.
    • (1981) J. Heredity , vol.72 , pp. 128
    • Chernoff, G.1
  • 16
    • 0022413538 scopus 로고
    • Chromosomal mapping of mouse myelin basic protein gene and structure and transcription of the partially deleted gene in shiverer mutant mice
    • Roach A., Takahashi N., Pravtcheva D., Ruddie F., Hood L. Chromosomal mapping of mouse myelin basic protein gene and structure and transcription of the partially deleted gene in shiverer mutant mice. Cell. 42:1985;149-155.
    • (1985) Cell , vol.42 , pp. 149-155
    • Roach, A.1    Takahashi, N.2    Pravtcheva, D.3    Ruddie, F.4    Hood, L.5
  • 17
    • 0024430148 scopus 로고
    • Myelin-deficient rat: A point mutation in exon III (A-C, Thr75-Pro)
    • Boison D., Stoffel W. Myelin-deficient rat: a point mutation in exon III (A-C, Thr75-Pro). EMBO J. 8:1989;3295-3302.
    • (1989) EMBO J. , vol.8 , pp. 3295-3302
    • Boison, D.1    Stoffel, W.2
  • 19
    • 0032518366 scopus 로고    scopus 로고
    • Myelin associated glycoprotein modulates glia-axon contact in vivo
    • Li C., Trapp B., Ludwin S., Peterson A., Roder J. Myelin associated glycoprotein modulates glia-axon contact in vivo. J. Neurosci. Res. 51:1998;210-217.
    • (1998) J. Neurosci. Res. , vol.51 , pp. 210-217
    • Li, C.1    Trapp, B.2    Ludwin, S.3    Peterson, A.4    Roder, J.5
  • 20
    • 0026615047 scopus 로고
    • Mouse P0 gene disruption leads to hypomyelination, abnormal expression of recognition molecules, and degeneration of myelin and axons
    • Giese K.P., Martini R., Lemke G., Soriano P., Schachner M. Mouse P0 gene disruption leads to hypomyelination, abnormal expression of recognition molecules, and degeneration of myelin and axons. Cell. 71:1992;565-576.
    • (1992) Cell , vol.71 , pp. 565-576
    • Giese, K.P.1    Martini, R.2    Lemke, G.3    Soriano, P.4    Schachner, M.5
  • 21
    • 0030850760 scopus 로고    scopus 로고
    • Functional analysis in vivo of the double mutant mouse deficient in both proteolipid protein and myelin basic protein in central nervous system
    • Stoffel W., Boison D., Büssow H. Functional analysis in vivo of the double mutant mouse deficient in both proteolipid protein and myelin basic protein in central nervous system. Cell Tissue Res. 289:1997;195-206.
    • (1997) Cell Tissue Res. , vol.289 , pp. 195-206
    • Stoffel, W.1    Boison, D.2    Büssow, H.3
  • 22
    • 0343953472 scopus 로고    scopus 로고
    • Early onset of axonal degeneration in double (plp-/-mag-/-) and hypomyelinosis in triple (plp-/-mbp-/-mag-/-) mutant mice
    • Uschkureit T., Sporkel O., Stracke J., Bussow H., Stoffel W. Early onset of axonal degeneration in double (plp-/-mag-/-) and hypomyelinosis in triple (plp-/-mbp-/-mag-/-) mutant mice. J. Neurosci. 20:2000;5225-5233.
    • (2000) J. Neurosci. , vol.20 , pp. 5225-5233
    • Uschkureit, T.1    Sporkel, O.2    Stracke, J.3    Bussow, H.4    Stoffel, W.5
  • 23
    • 0028849016 scopus 로고
    • UDP galactose: Ceramide galactosyltransferase and glutamate/aspartate transporter. Copurification, separation and characterization of the two glycoproteins
    • Schulte S., Stoffel W. UDP galactose: ceramide galactosyltransferase and glutamate/aspartate transporter. Copurification, separation and characterization of the two glycoproteins. Eur. J. Biochem. 233:1995;947-953.
    • (1995) Eur. J. Biochem. , vol.233 , pp. 947-953
    • Schulte, S.1    Stoffel, W.2
  • 24
    • 0031982356 scopus 로고    scopus 로고
    • Galactosphingolipids and axono-glial interaction in myelin of central nervous system
    • Bosio A., Büssow H., Adam J., Stoffel W. Galactosphingolipids and axono-glial interaction in myelin of central nervous system. Cell Tissue Res. 292:1998;199-210.
    • (1998) Cell Tissue Res. , vol.292 , pp. 199-210
    • Bosio, A.1    Büssow, H.2    Adam, J.3    Stoffel, W.4


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.