Thalamic involvement in a spinocerebellar ataxia type 2 (SCA2) and a spinocerebellar ataxia type 3 (SCA3) patient, and its clinical relevance

Brain

Volumn 126, Issue 10, 2003, Pages 2257-2272

  Rüb, Udo ^a   Del Turco, D ^a   Del Tredici, K ^a   De Vos, R A I ^c   Brunt, E R ^d   Reifenberger, G ^b   Seifried, C ^a   Schultz, C ^a   Auburger, G ^a   Braak, H ^a  

^a GOETHE UNIVERSITY   (Germany)

^b HEINRICH HEINE UNIVERSITY   (Germany)

^c Laboratorium Pathologie Oost Nederland   (Netherlands)

^d UNIVERSITY MEDICAL CENTER GRONINGEN   (Netherlands)

Author keywords

Machado Joseph disease; Pathoanatomy; Polyglutamine diseases; Spinocerebellar ataxias; Thalamus

Indexed keywords

LIPOFUSCIN;

ADOLESCENT; ADULT; AGED; ARTICLE; ATAXIA; BRADYKINESIA; CLINICAL ARTICLE; DYSARTHRIA; DYSDIADOCHOKINESIA; DYSKINESIA; EVOKED VISUAL RESPONSE; FALLING; FEMALE; GAIT; HUMAN; HUMAN TISSUE; LATERAL GENICULATE BODY; MALE; NERVE DEGENERATION; NISSL SUBSTANCE; PATHOLOGICAL ANATOMY; PRIORITY JOURNAL; PULVINAR; RETICULAR FORMATION; SACCADIC EYE MOVEMENT; SOMATOSENSORY DISORDER; SPINOCEREBELLAR ATAXIA TYPE 2; SPINOCEREBELLAR ATAXIA TYPE 3; SPINOCEREBELLAR DEGENERATION; STANDING; THALAMOCORTICAL TRACT; THALAMUS; THALAMUS ANTERIOR NUCLEUS; THALAMUS DORSOMEDIAL NUCLEUS; THALAMUS LATERAL NUCLEUS; THALAMUS POSTERIOR NUCLEUS; THALAMUS VENTRAL NUCLEUS; CASE REPORT; CHEMISTRY; GENETICS; METABOLISM; PATHOLOGY; REVIEW;

ADOLESCENT; AGED; FEMALE; HUMANS; LIPOFUSCIN; NISSL BODIES; SPINOCEREBELLAR ATAXIAS; THALAMUS;

EID: 0242336434     PISSN: 00068950     EISSN: None     Source Type: Journal    
DOI: 10.1093/brain/awg234     Document Type: Article

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