Optimal dietary therapy of long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency

Molecular Genetics and Metabolism

Volumn 79, Issue 2, 2003, Pages 114-123

  Gillingham, Melanie B ^a   Connor, William E ^b   Matern, Dietrich ^c   Rinaldo, Piero ^c   Burlingame, Terry ^a   Meeuws, Kaatje ^b   Harding, Cary O ^a  

^a OREGON HEALTH AND SCIENCE UNIVERSITY   (United States)

^b OREGON HEALTH AND SCIENCE UNIVERSITY   (United States)

^c Dept of Lab Med and Pathology   (United States)

Author keywords

Acylcarnitines; Essential fatty acids; Long chain 3 hydroxyacyl CoA dehydrogenase deficiency; Long chain fatty acids; Medium chain triglycerides; Trifunctional protein deficiency

Indexed keywords

3 HYDROXYACYL COENZYME A DEHYDROGENASE; ACYLCARNITINE; ALPHA TOCOPHEROL; CARBOHYDRATE; CARBOXYLIC ACID; CARNITINE; ESSENTIAL FATTY ACID; LINOLEIC ACID; LINOLENIC ACID; LONG CHAIN FATTY ACID; MEDIUM CHAIN FATTY ACID; PALMITOLEIC ACID; RICINOLEIC ACID; VITAMIN K GROUP;

3 HYDROXYLACYL COENZYME A DEHYDROGENASE DEFICIENCY; ARTICLE; CALORIC INTAKE; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; CORRELATION ANALYSIS; DIET SUPPLEMENTATION; DIET THERAPY; DIETARY INTAKE; ENZYME DEFICIENCY; FAT INTAKE; FATTY ACID BLOOD LEVEL; FEMALE; FOLLOW UP; HUMAN; MALE; PRIORITY JOURNAL; VITAMIN SUPPLEMENTATION;

EID: 0038617400     PISSN: 10967192     EISSN: None     Source Type: Journal    
DOI: 10.1016/S1096-7192(03)00073-8     Document Type: Article

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