Abnormal trafficking of sarcolemmal proteins in α-glucosidase deficiency

Acta Neuropathologica

Volumn 105, Issue 4, 2003, Pages 373-380

  Radojevic, V ^a   Humm, A M ^a   Rosler K M ^a   Lauterburg, T ^a   Burgunder, J M ^a,b  

^a UNIVERSITY OF BERN   (Switzerland)

^b NATIONAL NEUROSCIENCE INSTITUTE   (Singapore)

Author keywords

Cell culture; Organelle; Trafficking; Glucosidase

Indexed keywords

ALPHA GLUCOSIDASE; DYSTROPHIN; GLYCOGEN; MUSCLE PROTEIN; SARCOGLYCAN; UTROPHIN; CYTOSKELETON PROTEIN; MEMBRANE PROTEIN;

ADULT; ARTICLE; CASE REPORT; CELL CULTURE; CELL VACUOLE; ENZYME DEFICIENCY; GLYCOGEN MUSCLE LEVEL; GOLGI COMPLEX; HISTOPATHOLOGY; HUMAN; HUMAN CELL; HUMAN TISSUE; MALE; MUSCLE CELL; MUSCLE FIBRIL; MYOPATHY; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN LOCALIZATION; PROTEIN METABOLISM; SARCOLEMMA; SARCOPLASM; SARCOPLASMIC RETICULUM; UPREGULATION; GLYCOGEN STORAGE DISEASE TYPE 2; IMMUNOHISTOCHEMISTRY; METABOLISM; MIDDLE AGED; PATHOLOGY; PATHOPHYSIOLOGY; PHYSIOLOGY; PROTEIN TRANSPORT; SKELETAL MUSCLE;

CELLS, CULTURED; CYTOSKELETAL PROTEINS; DYSTROPHIN; GLYCOGEN STORAGE DISEASE TYPE II; HUMANS; IMMUNOHISTOCHEMISTRY; MALE; MEMBRANE PROTEINS; MIDDLE AGED; MUSCLE, SKELETAL; PROTEIN TRANSPORT; UTROPHIN; VACUOLES;

EID: 0037775817     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00401-002-0656-z     Document Type: Article

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