Transport of Trembler-J mutant peripheral myelin protein 22 is blocked in the intermediate compartment and affects the transport of the wild-type protein by direct interaction

Journal of Neuroscience

Volumn 19, Issue 6, 1999, Pages 2027-2036

  Tobler, Andreas R ^a   Notterpek, Lucia ^b   Naef, Roland ^a   Taylor, Verdon ^b   Suter, Ueli ^a   Shooter, Eric M ^c  

^a STANFORD UNIVERSITY   (United States)

^b ETH ZURICH   (Switzerland)

^c STANFORD UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

Dimerization; Epitope tag; Intermediate compartment; Myelin; Peripheral neuropathy; PMP22; Protein trafficking; Schwann cells; Trembler J mouse

Indexed keywords

EPITOPE; MUTANT PROTEIN; MYELIN PROTEIN; PROTEIN;

ANIMAL CELL; ARTICLE; CELLULAR DISTRIBUTION; DIMERIZATION; DISEASE ASSOCIATION; GENE DELETION; GENE DUPLICATION; HEREDITARY MOTOR SENSORY NEUROPATHY; MOLECULAR CLONING; MORPHOGENESIS; MOUSE; MYELINATION; NONHUMAN; PERIPHERAL NEUROPATHY; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN EXPRESSION; PROTEIN INTERACTION; PROTEIN STRUCTURE; PROTEIN TRANSPORT; SCHWANN CELL;

EID: 0033559844     PISSN: 02706474     EISSN: None     Source Type: Journal    
DOI: 10.1523/jneurosci.19-06-02027.1999     Document Type: Article

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